Gonçalves Elias, Sachicola Ofélia, Estanislau Bartolomeu, Quifica Francisca, Morais Humberto, Arrais Margarete
Serviço de Pneumologia Complexo Hospitalar de Doenças Cardiopulmonares, Cardeal Dom Alexandre do Nascimento Luanda Angola.
Centro de Estudos Avançados em Educação e Formação Médica, Faculdade de Medicina Agostinho Neto University Luanda Angola.
Clin Case Rep. 2023 Oct 19;11(10):e8107. doi: 10.1002/ccr3.8107. eCollection 2023 Oct.
Pulmonary agenesis is a rare congenital abnormality. Patients with hemithorax white-out on x-rays should be treated with caution, especially in resource-limited countries where chest CT and bronchofibroscopy are not available to confirm the diagnosis.
Pulmonary agenesis is an uncommon congenital abnormality defined by the complete absence of the lung parenchyma, as well as the bronchial and vascular structures. Right-sided pulmonary agenesis is less frequent, has a worse prognosis, and is usually associated with other congenital abnormalities. We reported the clinical case of a 31-year-old woman with right pulmonary agenesis, and no other congenital abnormalities, whose diagnosis was confirmed by thoracic computed tomography and bronchofibroscopy and who has a good prognosis.
肺不发育是一种罕见的先天性异常。胸部X线显示半侧胸腔呈白色致密影的患者应谨慎处理，尤其是在资源有限、无法进行胸部CT和支气管纤维镜检查以确诊的国家。
肺不发育是一种罕见的先天性异常，其定义为肺实质、支气管和血管结构完全缺失。右侧肺不发育较为少见，预后较差，且通常与其他先天性异常相关。我们报告了一例31岁女性右侧肺不发育且无其他先天性异常的临床病例，其诊断经胸部计算机断层扫描和支气管纤维镜检查得以证实，预后良好。
