Department of Urology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK.
Department of Paediatric Surgery, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK.
Pediatr Surg Int. 2023 Nov 16;39(1):293. doi: 10.1007/s00383-023-05564-1.
Cloacal malformation is a rare anomaly that remains a diagnostic challenge prenatally, despite the current advances in ultrasonography and MRI. This condition can in some, present with isolated ascites or with other findings, such as a pelvic cyst or upper urinary tract dilatation. In a minority, the ascites may be progressive, questioning the role of antenatal intervention.
We report on ten patients that have been identified from our Cloaca database between 2010 and 2022.
The presence of ascites was associated with extensive bowel adhesions and matting, leading to a challenging initial laparotomy and peri-operative course.
Antenatal finding of ascites in newborns with cloacal malformations should raise a red flag. The surgeon and anaesthetist should be prepared for the operative difficulties secondary to bowel adhesions and the higher risk of haemodynamic instability at the initial surgery. An experienced team at initial laparotomy in such patients is vital.
II.
肛门直肠畸形是一种罕见的异常,尽管目前超声和 MRI 技术有了进步,但在产前仍然是一个诊断难题。这种情况在某些情况下可能表现为单纯性腹水,或者伴有其他发现,如盆腔囊肿或上尿路扩张。在少数情况下,腹水可能会逐渐加重,这就引发了对产前干预作用的质疑。
我们从 2010 年至 2022 年的 Cloaca 数据库中确定了 10 名患者。
腹水的存在与广泛的肠粘连和粘连有关,导致初始剖腹手术和围手术期过程极具挑战性。
对于患有肛门直肠畸形的新生儿,产前发现腹水应引起警惕。外科医生和麻醉师应该为继发于肠粘连的手术困难以及初始手术时血液动力学不稳定的更高风险做好准备。在这些患者中,经验丰富的初始剖腹手术团队至关重要。
II 级。