Brauman A, Gilboa Y
Arch Intern Med. 1987 Feb;147(2):378-9.
Recurrent attacks of pulmonary atelectasis were the leading sign of familial Mediterranean fever in a young man of Jewish-Georgian extraction. His mother suffered from the more common manifestations of the disease. Treatment with colchicine caused a complete disappearance of his attacks. However, when challenged by discontinuing colchicine therapy for eight days, another, documented attack of pulmonary atelectasis occurred. To our knowledge, this is the first case of familial Mediterranean fever presenting with recurrent pulmonary atelectasis.
复发性肺不张发作是一名具有犹太 - 格鲁吉亚血统的年轻男子家族性地中海热的主要症状。他的母亲患有该病更常见的表现形式。秋水仙碱治疗使他的发作完全消失。然而,当停用秋水仙碱治疗八天进行激发试验时,又发生了一次有记录的肺不张发作。据我们所知,这是首例以复发性肺不张为表现的家族性地中海热病例。