Internal Medicine, Tulane University School of Medicine, New Orleans, Louisiana, USA
Internal Medicine, NYU Grossman School of Medicine, New York, New York, USA.
BMJ Case Rep. 2024 Jan 5;17(1):e258084. doi: 10.1136/bcr-2023-258084.
Pulmonary artery intimal sarcomas (PAISs) are rare, malignant tumours that arise from the intimal or intramural wall of the pulmonary artery and are often mistaken for pulmonary emboli. Diagnosis and treatment of this condition are difficult due to the lack of formal guidelines. Initiating treatment as soon as possible after diagnosis is essential for maximising survival. Here, we present the case of a patient with a PAIS that initially presented similar to pulmonary thromboembolic disease and was treated with a multimodal approach.
肺动脉内膜肉瘤（PAISs）是一种罕见的恶性肿瘤，起源于肺动脉的内膜或壁内，常被误诊为肺栓塞。由于缺乏正式的指南，这种疾病的诊断和治疗都很困难。在诊断后尽快开始治疗对于最大限度地提高生存率至关重要。在这里，我们介绍了一个 PAIS 患者的病例，该患者最初表现类似于肺血栓栓塞性疾病，并采用了多模式治疗。
