Urology, Royal United Hospital Bath NHS Trust, Bath, UK
University Hospitals Bristol and Weston NHS Foundation Trust, Bristol, UK.
BMJ Case Rep. 2024 Jan 29;17(1):e257922. doi: 10.1136/bcr-2023-257922.
A girl in early adolescence with autism presented with 3 months of abdominal pain and 36 hours of anuria. She had recently received treatment for urinary tract infections, anxiety and menorrhagia (she had undergone menarche a few months earlier). Due to the pain, she had pulled out an incisor. Bladder scan showed 923 mL, creatinine was 829 mmol/L but urethral catheter insertion did not drain urine. An unenhanced CT scan revealed an absent left kidney, didelphys uterus and right-sided hydroureteronephrosis caused by haematocolpos in keeping with a diagnosis of OHVIRA syndrome and ureteric obstruction of a single kidney causing acute renal failure. She underwent vaginal septoplasty, drainage of the haematocolpos and right ureteric stent.
一名早青春期的自闭症女孩因腹痛 3 个月和无尿 36 小时就诊。她最近因尿路感染、焦虑和月经过多（几个月前初潮）接受了治疗。由于疼痛，她拔掉了一颗门牙。膀胱扫描显示 923 毫升，肌酐为 829mmol/L，但尿道导管插入术未引出尿液。未增强 CT 扫描显示左肾缺失、双子宫和右侧肾盂积水，符合 OHVIRA 综合征的诊断，且单肾输尿管梗阻导致急性肾衰竭。她接受了阴道隔切开术、阴道积血引流术和右输尿管支架置入术。
