Tan Han Ling, Ahmad Tunku Sara, Sankara Kumar C, Khirusman Adnan Yohan, Looi Lai Meng, Gunasagaran Jayaletchumi
Department of Orthopaedic Surgery (NOCERAL), Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia.
Department of Pathology, Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia.
EFORT Open Rev. 2024 Feb 1;9(2):129-137. doi: 10.1530/EOR-23-0151.
Superficial acral fibromyxoma, also known as digital fibromyxoma, is a slow-growing, benign, solitary soft tissue tumor. First described in 2001 by Fetsch et al., it is a condition that often occurs in middle-aged individuals. However, it has also been reported across a wide range of ages, ranging from 4 to 86 years, with males more commonly reported. The condition often presents as solitary soft tissue swelling over the periungual or subungual. We present the management experience of the rare presentation of this rare tumor and a detailed review of the past literature on this condition. Detailed management of the condition has been described, along with the outcome after 2 years of follow-up and treatment experience. Our detailed analysis shows that 2 years is the shortest duration of follow-up to rule out recurrence. Hence, most of the cases reported earlier had given the false sense of the recurrence rate of the tumor, which could lead to undertreatment of the condition. The purpose of this article is to allow the readers to understand better the tumor's characteristics with bone involvement and the tumor's diagnostic strategies and treatment options.
浅表性肢端纤维黏液瘤,也称为指部纤维黏液瘤,是一种生长缓慢的良性孤立性软组织肿瘤。2001年由费奇等人首次描述,这种疾病常发生于中年个体。然而,各年龄段均有病例报道,年龄范围从4岁至86岁,男性病例更为常见。该疾病常表现为甲周或甲下的孤立性软组织肿胀。我们介绍了这种罕见肿瘤罕见表现的治疗经验,并对以往关于该疾病的文献进行了详细综述。文中描述了该疾病的详细治疗方法,以及2年随访后的结果和治疗经验。我们的详细分析表明,2年是排除复发的最短随访时间。因此,早期报道的大多数病例给人造成了肿瘤复发率的错误印象,这可能导致对该疾病的治疗不足。本文旨在让读者更好地了解该肿瘤合并骨受累的特征、诊断策略及治疗选择。