Hirata Akiko, Hayashi Akiteru, Yamazaki Shun, Hanada Hayato, Nakamura Syogo, Ogino Akihiro
From the Department of Plastic and Reconstructive Surgery, Toho University Ohashi Medical Center, Tokyo, Japan.
Department of Plastic and Reconstructive Surgery, Toho University Sakura Medical Center, Chiba, Japan.
Plast Reconstr Surg Glob Open. 2024 Feb 19;12(2):e5618. doi: 10.1097/GOX.0000000000005618. eCollection 2024 Feb.
Hereditary skin laxity is a rare condition, some cases of which are also referred to as cutis laxa, and those involving facial skin are considered a target for treatment by plastic surgery as patients present with an aged face, which can reduce their quality of life. In some of these patients, the facial nerve and muscles may be affected, and cause weakness of mimetic muscles. We performed one-stage bilateral lengthening temporalis myoplasty reanimation, followed by lower facial contouring with partial lower lip excision and hammock-shaped fascia grafting in two patients with hereditary facial skin laxity coexisting with facial palsy. The patient was a 63-year-old woman with hereditary gelsolin amyloidosis and a 64-year-old man who was diagnosed with oculopharyngeal muscular dystrophy. Postoperatively, a symmetrical facial contour was achieved in repose, and smiling with and without biting was possible. To our knowledge, there are no reports of dynamic smile reconstruction for facial weakness in patients with hereditary facial skin laxity. Although these patients may experience progressive loss of function of the trigeminal nerve and its innervating muscles, the static suspension effect of lengthening temporalis myoplasty can be expected to continue even if the temporal muscles lose their function in the future. We believe that, with careful patient selection, dynamic reconstruction is an option for progressive facial paralysis. In this article, we present the chronological history of two patients who underwent multiple plastic surgery procedures and discuss the importance of the role of plastic surgery in improving the quality of life under these conditions.
遗传性皮肤松弛症是一种罕见的病症,其中一些病例也被称为皮肤松弛症,而那些累及面部皮肤的病例被认为是整形外科的治疗对象,因为患者会出现面容老化,这会降低他们的生活质量。在这些患者中的一些人身上,面神经和肌肉可能会受到影响,导致表情肌无力。我们对两名患有遗传性面部皮肤松弛症并伴有面瘫的患者进行了一期双侧颞肌延长肌成形术重建,随后进行了下唇部分切除和吊床状筋膜移植的面部轮廓重塑。患者分别是一名患有遗传性凝溶胶蛋白淀粉样变性的63岁女性和一名被诊断患有眼咽型肌营养不良症的64岁男性。术后,患者在静息状态下实现了面部轮廓对称,并且能够进行有咬和无咬动作的微笑。据我们所知,尚无关于遗传性面部皮肤松弛症患者面部无力的动态微笑重建的报道。尽管这些患者可能会经历三叉神经及其支配肌肉的功能逐渐丧失,但即使颞肌未来失去功能,延长颞肌成形术的静态悬吊效果预计仍会持续。我们认为,经过仔细的患者选择,动态重建是进行性面瘫的一种选择。在本文中,我们介绍了两名接受多次整形手术的患者的病史,并讨论了整形手术在改善这些情况下生活质量方面的重要作用。