Billotte Maxime, Eszto Peter, Thomas Benoît, Groizard Pierre, Perez Pierre, Campagne Julien
Hôpital Robert Schuman Médecine Interne Vantoux France.
Réanimation Hôpital Robert Schuman Vantoux France.
EJHaem. 2024 Feb 11;5(1):225-230. doi: 10.1002/jha2.848. eCollection 2024 Feb.
Sarcoidosis is an inflammatory disease known to be associated with multiple autoimmune disorders. There is a restricted number of descriptions of the association between sarcoidosis and autoimmune thrombotic thrombocytopenic purpura (aTTP). We present the case of a 63-year-old woman admitted to the hospital to investigate a possible sarcoidosis who had hemolytic anemia and thrombocytopenia, with low ADAMTS13 activity and anti-ADAMTS13 antibodies, leading to a diagnosis of aTTP. Sarcoidosis was later confirmed and the two conditions evolved separately after 6 months, questioning the link between them. Clinicians should be aware of this rare cause of thrombocytopenia in patients with sarcoidosis, as aTTP is a life-threatening condition.
结节病是一种已知与多种自身免疫性疾病相关的炎症性疾病。关于结节病与自身免疫性血栓性血小板减少性紫癜(aTTP)之间关联的描述数量有限。我们报告了一例63岁女性患者,因可能患有结节病入院检查,该患者有溶血性贫血和血小板减少症,伴有低ADAMTS13活性和抗ADAMTS13抗体,最终诊断为aTTP。后来结节病得到确诊,6个月后这两种病症分别发展,这对它们之间的联系提出了质疑。临床医生应意识到结节病患者血小板减少症的这种罕见病因,因为aTTP是一种危及生命的疾病。