Khaoula Boumeriem, Iliass Bourekba, Nazik Allali, Latifa Chat, Siham El Haddad
Children's Hospital of Rabat, Morocco.
Glob Pediatr Health. 2024 Mar 3;11:2333794X241234733. doi: 10.1177/2333794X241234733. eCollection 2024.
Dyke Davidoff-Masson syndrome is a rare neurological condition that results from brain injury during early childhood stages. The precise incidence of this condition is unknown, with a slight male predominance, and adult forms have been documented. Imaging findings reveal hemisphere atrophy along with ipsilateral compensatory skull changes and hyper-pneumatization of mastoid cells. The treatment approach involves anti-epileptic medications and hemispherectomy is reserved for cases with intractable seizures. This case report delineates the clinical manifestation and therapeutic approach employed in an 8-year-old male patient exhibiting pharmaco-resistant left hemi-body convulsive seizures. The magnetic resonance imaging (MRI) findings revealed right cerebral hemiatrophy, mesencephalon atrophy, ipsilateral calvarial hypertrophy and hyperpneumatization of mastoid cells. The objective of this study is to contribute to the existing literature by presenting this rare case report. We propose that in cases involving pediatric pharmaco-resistant epilepsy, it is essential to conduct further investigations to establish a comprehensive management strategy.
戴克 - 大卫多夫 - 马森综合征是一种罕见的神经系统疾病，由儿童早期脑部损伤引起。这种疾病的确切发病率尚不清楚，男性略占优势，且已有成人病例的记录。影像学检查结果显示半球萎缩，同时伴有同侧颅骨的代偿性改变以及乳突细胞的过度气化。治疗方法包括使用抗癫痫药物，对于难治性癫痫病例则采用半球切除术。本病例报告描述了一名8岁男性患者的临床表现及治疗方法，该患者患有药物抵抗性左侧半身惊厥性癫痫。磁共振成像（MRI）检查结果显示右侧大脑半球萎缩、中脑萎缩、同侧颅骨肥厚以及乳突细胞过度气化。本研究的目的是通过呈现这一罕见病例报告为现有文献做出贡献。我们建议，在涉及儿童药物抵抗性癫痫的病例中，有必要进行进一步调查以制定全面的管理策略。
