Younas Amna, Saim Muhammad, Maqsood Hamza, Younus Shifa, Hassan Raza Muhammad
Medicine, Russells Hall Hospital, Dudley, GBR.
Department of Cardiology, Nishtar Medical University, Multan, PAK.
Cureus. 2020 Dec 5;12(12):e11919. doi: 10.7759/cureus.11919.
Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder that results from brain injury in intrauterine or early years of life. Prominent cortical sulci, dilated lateral ventricles, cerebral hemiatrophy, hyperpneumatization of the frontal sinus, and compensatory hypertrophy of the skull are the characteristic findings. We describe a male patient who presented with generalized tonic-clonic seizure and left-sided body weakness and neuroimaging findings of cerebral hemiatrophy, dilatation of right lateral ventricle, right frontal sinus hyperpneumatization, and asymmetric calvarial thickening. Knowledge of its features on imaging enables timely and accurate diagnosis, allowing appropriate management.
戴克-戴维多夫-马森综合征（DDMS）是一种罕见的神经系统疾病，由子宫内或生命早期的脑损伤引起。显著的脑沟、侧脑室扩张、大脑半球萎缩、额窦过度气化以及颅骨代偿性增厚是其特征性表现。我们描述了一名男性患者，他出现全身性强直阵挛发作和左侧身体无力，神经影像学表现为大脑半球萎缩、右侧侧脑室扩张、右侧额窦过度气化以及颅骨不对称增厚。了解其影像学特征有助于及时准确诊断，从而进行适当的治疗。
