Peyrottes Arthur, Bodard Sylvain, Timsit Marc-Olivier, Méjean Arnaud, Panthier Frederic, Audenet François
Service d'Urologie, Hôpital Européen Georges-Pompidou, AP-HP Centre, Université Paris Cité, 20, rue Leblanc, 75015 Paris, France.
Service d'Imagerie Adulte, Hôpital Necker-Enfants-Malades, AP-HP Centre, Université Paris Cité, Paris, France; Sorbonne Université, CNRS UMR 7371, Inserm U 1146, Laboratoire d'Imagerie Biomédicale (LIB), 75006 Paris, France.
Fr J Urol. 2024 Mar 8;34(4):102609. doi: 10.1016/j.fjurol.2024.102609.
Angiosarcoma is a rare malignancy derived from endothelial cells, which behaves aggressively. Primary angiosarcoma of the kidney is even rarer, and its clinical and radiological presentations do not differ from clear cells renal cell carcinoma (ccRCC). Management protocols are not standardized, although nephrectomy is usually performed. Subsequent treatments (chemotherapy, radiotherapy, and lately, targeted therapies) vary considerably. Herein, we report the case of a middle-aged patient harboring primary angiosarcoma of the left kidney and discuss its presentation and management in light of current guidelines. The case is described for its rarity and masquerading nature.
