Bajpai Jyoti, Verma Shreya, Kant Surya, Verma Ajay Kumar, Bajaj Darshan, Pradhan Akshyaya, Bhalla Shalini
Department of Respiratory Medicine, King George's Medical University, Lucknow, Uttar Pradesh, India.
Department of Faculty of Medical Sciences, King George's Medical University, Lucknow, Uttar Pradesh, India.
Int J Appl Basic Med Res. 2024 Jan-Mar;14(1):67-69. doi: 10.4103/ijabmr.ijabmr_376_23. Epub 2024 Feb 20.
Pulmonary sequestration and cystic pulmonary adenomatoid malformation are rare congenital cystic disorders of the lungs. The presence of both the diseases in the same individual is therefore very uncommon. Pulmonary sequestration is a nonfunctional pulmonary tissue mass that derives its blood supply from systemic blood supply other than pulmonary circulation. Congenital cystic pulmonary adenomatoid malformation represents a mass consisting of abnormal bronchiolar air spaces and a deficiency of functional alveoli. This is the case report of a 9-year-old girl with intermittent fever, left-sided chest pain, and cough for the past 15 days along with recurrent coughs since childhood suggestive of hybrid pulmonary sequestration, congenital cystic adenomatoid malformation, and dextrocardia.
肺隔离症和先天性囊性腺瘤样畸形是罕见的先天性肺部囊性疾病。因此,同一个体同时存在这两种疾病的情况非常少见。肺隔离症是一种无功能的肺组织团块,其血供来自肺循环以外的体循环。先天性囊性腺瘤样畸形表现为一个由异常细支气管气腔和功能性肺泡缺乏组成的团块。这是一例9岁女孩的病例报告,该女孩在过去15天里出现间歇性发热、左侧胸痛和咳嗽,并且自童年起就反复咳嗽,提示合并肺隔离症、先天性囊性腺瘤样畸形和右位心。