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达那唑治疗获得性无巨核细胞性血小板减少性紫癜:一例报告

Danazol in acquired amegakaryocytic thrombocytopenic purpura: a case report.

作者信息

Kayser W, Euler H H, Schmitz N, Gassmann W, Löffler H, Asbeck F

出版信息

Blut. 1985 Dec;51(6):401-4. doi: 10.1007/BF00320726.

DOI:10.1007/BF00320726
PMID:3852685
Abstract

Acquired amegakaryocytic thrombocytopenic purpura is a rare disease. Most reported patients did not respond to any therapeutical approach. Recently we observed a striking improvement of this disorder in a female patient shortly after therapy with danazol had been initiated. This observation and its possible implication for the treatment of amegakaryocytic thrombocytopenia are reported herein.

摘要

获得性无巨核细胞性血小板减少性紫癜是一种罕见疾病。大多数报道的患者对任何治疗方法均无反应。最近,我们观察到一名女性患者在开始使用达那唑治疗后不久,这种疾病有显著改善。本文报告了这一观察结果及其对无巨核细胞性血小板减少症治疗的可能意义。

相似文献

1
Danazol in acquired amegakaryocytic thrombocytopenic purpura: a case report.达那唑治疗获得性无巨核细胞性血小板减少性紫癜:一例报告
Blut. 1985 Dec;51(6):401-4. doi: 10.1007/BF00320726.
2
The use of danazol in the management of chronic immune thrombocytopenic purpura.达那唑在慢性免疫性血小板减少性紫癜治疗中的应用。
Br J Haematol. 1985 Sep;61(1):145-8. doi: 10.1111/j.1365-2141.1985.tb04070.x.
3
Danazol therapy in refractory chronic immune thrombocytopenic purpura.达那唑治疗难治性慢性免疫性血小板减少性紫癜。
Acta Haematol. 1987;77(1):45-7. doi: 10.1159/000205948.
4
Danazol in chronic idiopathic thrombocytopenic purpura resistant to corticosteroids.达那唑用于对皮质类固醇耐药的慢性特发性血小板减少性紫癜。
Folia Haematol Int Mag Klin Morphol Blutforsch. 1987;114(6):768-76.
5
Danazol for the treatment of idiopathic thrombocytopenic purpura.达那唑用于治疗特发性血小板减少性紫癜。
N Engl J Med. 1983 Jun 9;308(23):1396-9. doi: 10.1056/NEJM198306093082306.
6
Danazol therapy in cyclic acquired amegakaryocytic thrombocytopenic purpura: a case report.达那唑治疗周期性获得性无巨核细胞性血小板减少性紫癜:一例报告。
Am J Hematol. 1999 Mar;60(3):225-8. doi: 10.1002/(sici)1096-8652(199903)60:3<225::aid-ajh10>3.0.co;2-s.
7
[Evaluation of danazol therapy in chronic refractory idiopathic thrombocytopenic purpura].[达那唑治疗慢性难治性特发性血小板减少性紫癜的评估]
Rinsho Ketsueki. 1986 Sep;27(9):1705-11.
8
Use of danazol in the management of chronic idiopathic thrombocytopenic purpura.达那唑在慢性特发性血小板减少性紫癜治疗中的应用。
Isr J Med Sci. 1985 May;21(5):418-20.
9
Danazol in refractory autoimmune thrombocytopenic purpura (ATP). A new therapeutic sequence.
Arch Invest Med (Mex). 1985 Jul-Sep;16(3):295-304.
10
Danazol for the treatment of idiopathic thrombocytopenic purpura.达那唑用于治疗特发性血小板减少性紫癜。
Acta Haematol. 1985;74(2):97-8. doi: 10.1159/000206176.

引用本文的文献

1
Danazol: an effective option in acquired amegakaryocytic thrombocytopaenic purpura.达那唑:获得性无巨核细胞性血小板减少性紫癜的一种有效治疗选择。
Case Rep Hematol. 2015;2015:171253. doi: 10.1155/2015/171253. Epub 2015 Apr 5.
2
Anti-CD20 Antibody is Effective in the Patient with Refractory Amegakaryocytic Thrombocytopenia, 25 Months Follow up.抗CD20抗体对难治性无巨核细胞性血小板减少症患者有效,随访25个月
Int J Hematol Oncol Stem Cell Res. 2014;8(2):41-4.
3
Good response to cyclosporin in a child with acquired thrombocytopenic purpura.

本文引用的文献

1
Thrombocytopenia with decreased megakaryocytes. Evaluation and prognosis.
Ann Intern Med. 1981 Feb;94(2):170-5. doi: 10.7326/0003-4819-94-2-170.
2
Acquired hypomegakaryocytic thrombocytopenic purpura. Occurrence in a patient with absent thrombopoietic stimulating factor.获得性低巨核细胞性血小板减少性紫癜。发生于一名缺乏血小板生成刺激因子的患者。
Arch Intern Med. 1980 May;140(5):721-3. doi: 10.1001/archinte.140.5.721.
3
Acquired amegakaryocytic thrombocytopenic purpura: a syndrome of diverse etiologies.获得性无巨核细胞性血小板减少性紫癜:一种病因多样的综合征。
儿童获得性血小板减少性紫癜对环孢素反应良好。
Indian J Pediatr. 2012 Sep;79(9):1236-7. doi: 10.1007/s12098-011-0656-x. Epub 2011 Dec 15.
Blood. 1982 Nov;60(5):1173-8.
4
Danazol for the treatment of idiopathic thrombocytopenic purpura.达那唑用于治疗特发性血小板减少性紫癜。
N Engl J Med. 1983 Jun 9;308(23):1396-9. doi: 10.1056/NEJM198306093082306.
5
Successful treatment of amegakaryocytic thrombocytopenic purpura with cyclosporine.环孢素成功治疗无巨核细胞性血小板减少性紫癜。
N Engl J Med. 1985 Apr 18;312(16):1060-1.