Servicio de Neurociencias, Universidad de Buenos Aires, Instituto Cardiológico Banfield, Buenos Aires, Argentina.
Department of Psychiatry, Psychotherapy, Psychosomatics and Medical Psychology, Division of Psychiatry I, Medical University Innsbruck, Innsbruck, Austria.
J Med Life. 2023 Dec;16(12):1750-1755. doi: 10.25122/jml-2023-0459.
Amyotrophic lateral sclerosis (ALS) is a devastating and progressive neurodegenerative disease with limited treatment options available. Cerebrolysin is a drug candidate for the treatment of ALS because of its neuroprotective and neuroregenerative effects. We initiated a pilot clinical study of a combination of Cerebrolysin and riluzole to assess the therapeutic benefit of Cerebrolysin as an add-on treatment on clinical signs and symptoms in outpatients with ALS. Twenty patients with a clinically definitive diagnosis of ALS were enrolled and randomly assigned in a 1:1 ratio to receive Cerebrolysin or placebo. All patients received 50 mg of riluzole PO twice daily as a standard treatment. Patients in the Cerebrolysin group received intravenous injections of 10 mL of Cerebrolysin once daily, five days a week for the first month and three days a week for the next two months. Analysis of the ALS Functional Rating Scale - revised at Month 1 (primary outcome measure), showed a significant treatment effect in favor of Cerebrolysin with a 2.3-point improvement from baseline to Month 1 compared to a 0.9-point decrease in patients on placebo (P=0.005). The effect was maintained over the three-month study period, and the beneficial effect of Cerebrolysin over placebo was also evident in the secondary outcome measures. The safety analysis showed that the combination of riluzole and Cerebrolyisn was well tolerated. Our results demonstrate for the first time a significant clinical effect of Cerebrolysin in improving functional outcomes in patients with ALS and suggest that Cerebrolysin has potential as a novel therapeutic option for ALS.
肌萎缩侧索硬化症(ALS)是一种破坏性的进行性神经退行性疾病,治疗选择有限。脑活素是一种治疗 ALS 的候选药物,因为它具有神经保护和神经再生作用。我们启动了一项脑活素联合利鲁唑治疗 ALS 的试点临床研究,以评估脑活素作为附加治疗对门诊 ALS 患者临床症状的治疗益处。20 名具有明确临床诊断的 ALS 患者被纳入并随机分为 1:1 比例接受脑活素或安慰剂治疗。所有患者均接受 50mg 利鲁唑 PO,每日两次作为标准治疗。脑活素组患者接受 10ml 脑活素静脉注射,每日一次,第一个月连续 5 天,接下来两个月连续 3 天。对 1 个月时 ALS 功能评定量表修订版(主要终点测量)的分析显示,脑活素治疗有显著的治疗效果,与安慰剂组相比,从基线到 1 个月时的改善幅度为 2.3 点,而安慰剂组的下降幅度为 0.9 点(P=0.005)。这种效果在 3 个月的研究期间得以维持,并且脑活素的有益效果在次要终点测量中也很明显。安全性分析显示,利鲁唑和脑活素联合使用耐受性良好。我们的结果首次证明脑活素在改善 ALS 患者的功能结局方面具有显著的临床效果,并表明脑活素作为一种新型治疗选择具有治疗 ALS 的潜力。