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Myasthenia Gravis Associated With SARS-CoV-2 Infection.与严重急性呼吸综合征冠状病毒2型感染相关的重症肌无力
Ann Intern Med. 2020 Dec 15;173(12):1027-1028. doi: 10.7326/L20-0845. Epub 2020 Aug 10.
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Incidence and Ocular Features of Pediatric Myasthenias.小儿重症肌无力的发病情况和眼部特征。
Am J Ophthalmol. 2019 Apr;200:242-249. doi: 10.1016/j.ajo.2019.01.004. Epub 2019 Jan 14.
3
Serial Stimulated Jitter Analysis In Juvenile Myasthenia Gravis.成串刺激颤搐分析在青少年重症肌无力中的应用。
Muscle Nerve. 2018 Nov;58(5):729-732. doi: 10.1002/mus.26319. Epub 2018 Oct 2.
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Ocular myasthenia gravis: a review.眼肌型重症肌无力:综述
Indian J Ophthalmol. 2014 Oct;62(10):985-91. doi: 10.4103/0301-4738.145987.
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Juvenile myasthenia gravis: recommendations for diagnostic approaches and treatment.青少年重症肌无力:诊断方法与治疗建议
Neuropediatrics. 2014 Apr;45(2):75-83. doi: 10.1055/s-0033-1364181. Epub 2014 Jan 27.
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Update on juvenile myasthenia gravis.青少年重症肌无力的最新进展。
Curr Opin Pediatr. 2013 Dec;25(6):694-700. doi: 10.1097/MOP.0b013e328365ad16.
7
Juvenile myasthenia gravis: a paediatric perspective.青少年重症肌无力:儿科视角
Autoimmune Dis. 2011;2011:404101. doi: 10.4061/2011/404101. Epub 2011 Nov 1.
8
Anti-LRP4 autoantibodies in AChR- and MuSK-antibody-negative myasthenia gravis.抗 LRP4 自身抗体在乙酰胆碱受体抗体和肌肉特异性激酶抗体阴性的重症肌无力中的作用。
J Neurol. 2012 Mar;259(3):427-35. doi: 10.1007/s00415-011-6194-7. Epub 2011 Aug 5.
9
The ice pack test in the differential diagnosis of myasthenic diplopia.冰袋试验在重症肌无力性复视鉴别诊断中的应用
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10
Neurophysiological strategies for the diagnosis of disorders of the neuromuscular junction in children.儿童神经肌肉接头疾病诊断的神经生理学策略
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儿童眼肌型重症肌无力:两例报告。

Juvenile ocular myasthenia gravis: a report of two cases.

机构信息

University of South Carolina / Prisma Health, Columbia, South Carolina.

University of South Carolina School of Medicine, Columbia, South Carolina.

出版信息

Digit J Ophthalmol. 2024 Feb 2;30(1):15-18. doi: 10.5693/djo.02.2023.09.002. eCollection 2024.

DOI:10.5693/djo.02.2023.09.002
PMID:38601901
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11001568/
Abstract

We report 2 cases of pediatric ocular myasthenia gravis. The first case was a 7-year-old girl who presented with bilateral ophthalmoplegia and ptosis that correlated with the onset of upper respiratory symptoms. Neuroimaging and acetylcholine receptor antibody testing were unremarkable. The ice pack test was positive. Symptoms greatly improved with pyridostigmine, with full resolution of ophthalmoplegia achieved by 8-month follow-up. The second case was a 4-year-old girl who presented emergently with ptosis and bilateral ophthalmoplegia. Acetylcholine receptor antibodies testing was positive. The patient was started on pyridostigmine and intravenous immunoglobulin and is scheduled to follow-up with pediatric ophthalmology in the outpatient setting.

摘要

我们报告 2 例儿科眼肌型重症肌无力。第一例是一位 7 岁女孩,因上呼吸道症状出现双侧眼肌瘫痪和上睑下垂。神经影像学和乙酰胆碱受体抗体检测无异常。冰袋试验阳性。吡啶斯的明治疗后症状明显改善,随访 8 个月时眼肌瘫痪完全缓解。第二例是一位 4 岁女孩,因眼睑下垂和双侧眼肌瘫痪紧急就诊。乙酰胆碱受体抗体检测阳性。患者开始服用吡啶斯的明和静脉注射免疫球蛋白,并计划在门诊接受儿科眼科随访。