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儿童眼肌型重症肌无力:两例报告。

Juvenile ocular myasthenia gravis: a report of two cases.

机构信息

University of South Carolina / Prisma Health, Columbia, South Carolina.

University of South Carolina School of Medicine, Columbia, South Carolina.

出版信息

Digit J Ophthalmol. 2024 Feb 2;30(1):15-18. doi: 10.5693/djo.02.2023.09.002. eCollection 2024.

Abstract

We report 2 cases of pediatric ocular myasthenia gravis. The first case was a 7-year-old girl who presented with bilateral ophthalmoplegia and ptosis that correlated with the onset of upper respiratory symptoms. Neuroimaging and acetylcholine receptor antibody testing were unremarkable. The ice pack test was positive. Symptoms greatly improved with pyridostigmine, with full resolution of ophthalmoplegia achieved by 8-month follow-up. The second case was a 4-year-old girl who presented emergently with ptosis and bilateral ophthalmoplegia. Acetylcholine receptor antibodies testing was positive. The patient was started on pyridostigmine and intravenous immunoglobulin and is scheduled to follow-up with pediatric ophthalmology in the outpatient setting.

摘要

我们报告 2 例儿科眼肌型重症肌无力。第一例是一位 7 岁女孩,因上呼吸道症状出现双侧眼肌瘫痪和上睑下垂。神经影像学和乙酰胆碱受体抗体检测无异常。冰袋试验阳性。吡啶斯的明治疗后症状明显改善,随访 8 个月时眼肌瘫痪完全缓解。第二例是一位 4 岁女孩,因眼睑下垂和双侧眼肌瘫痪紧急就诊。乙酰胆碱受体抗体检测阳性。患者开始服用吡啶斯的明和静脉注射免疫球蛋白,并计划在门诊接受儿科眼科随访。

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Juvenile ocular myasthenia gravis: a report of two cases.儿童眼肌型重症肌无力:两例报告。
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本文引用的文献

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Ocular myasthenia gravis: a review.眼肌型重症肌无力:综述
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