Babaei Kiana, Rahnama Ali, Shurvarzi Nora, Movahedi Ali
Department of Anesthesia Neyshabur University of Medical Sciences Neyshabur Iran.
Department of Plastic Surgery Hakim Hospital, Neyshabur University of Medical Sciences Neyshabur Iran.
Clin Case Rep. 2024 Apr 30;12(5):e8878. doi: 10.1002/ccr3.8878. eCollection 2024 May.
Parry-Romberg syndrome is characterized by progressive dystrophy in one half of the face, which usually begins in childhood. Correct and timely diagnosis of this disease, as well as a multidisciplinary approach and timely surgical treatment to minimize the psychological effects and improve the patient's appearance are of particular importance.
Parry-Romberg syndrome is characterized by progressive dystrophy or loss of subcutaneous tissue in one half of the face, which usually begins in childhood and continues with skin changes, and can also be associated with linear scleroderma. Although this disease has been known for more than 150 years, its exact cause and pathogenesis are not well understood. The clinical feature of Parry-Romberg syndrome that makes it possible to diagnose is unilateral idiopathic facial atrophy. The reported case is a 14-year-old boy who suffered from hemifacial atrophy of the frontal area since he was 7 years old was referred to a plastic and cosmetic surgery specialist and underwent surgery without systemic symptoms and in the inactive phase of the disease. Correct and timely diagnosis of this disease, as well as a multidisciplinary approach and timely and appropriate surgical treatment to minimize the psychological effects and improve the patient's appearance are of particular importance.
帕里-龙贝格综合征的特征是面部一侧进行性萎缩，通常始于儿童期。正确及时地诊断该疾病，以及采用多学科方法并及时进行手术治疗以尽量减少心理影响并改善患者外观尤为重要。
帕里-龙贝格综合征的特征是面部一侧皮下组织进行性萎缩或丧失，通常始于儿童期并伴有皮肤变化，还可能与线状硬皮病相关。尽管这种疾病已被知晓150多年，但其确切病因和发病机制仍不清楚。帕里-龙贝格综合征能够被诊断的临床特征是单侧特发性面部萎缩。报告的病例是一名14岁男孩，自7岁起患有额部半侧面部萎缩，被转诊至整形美容外科专家处，在疾病无全身症状且处于静止期时接受了手术。正确及时地诊断该疾病，以及采用多学科方法并及时进行恰当的手术治疗以尽量减少心理影响并改善患者外观尤为重要。
