Department of Neonatology Nursing, West China Second University Hospital, Sichuan University, Chengdu, China.
Department of Nursing, West China Second University Hospital, Sichuan University, Chengdu, China.
BMC Pediatr. 2024 May 7;24(1):314. doi: 10.1186/s12887-024-04777-0.
Aplasia cutis congenita (ACC) is a congenital disorder that can be classified into nine types, with Type I ACC being the most common. Type V ACC associated with fetus papyraceus is a rare subtype of ACC. We report the case of a Type V ACC in a male newborn with extensive abdominal skin defects. The patient received conservative treatment using hydrogel foam and silicone foam dressings. Approximately five weeks later, the patient was discharged when more than 60% of the skin had completed epithelialization. After discharge from West China Second University Hospital, Chengdu , the patient continued to be followed up regularly at the Burns and Plastic Surgery Clinic at local hospital in Gansu. We followed up the child by telephone. After 4 months of follow-up, scar tissue formation was observed in the trunk area. The infant is 2 years and 5 months old now, physical examination did not reveal any organ problems.
先天性皮肤发育不全（ACC）是一种先天性疾病，可分为九种类型，其中 I 型 ACC 最为常见。与胎儿纸样骨相关的 V 型 ACC 是 ACC 的一种罕见亚型。我们报告了一例男性新生儿 V 型 ACC，其腹部广泛皮肤缺损。患者接受水凝胶泡沫和硅酮泡沫敷料的保守治疗。大约五周后，当超过 60%的皮肤完成上皮化时，患者出院。从成都华西第二医院出院后，患者继续在甘肃当地医院的烧伤整形科定期随访。我们通过电话对患儿进行随访。随访 4 个月后，观察到躯干区域有瘢痕组织形成。患儿现在 2 岁 5 个月，体格检查未发现任何器官问题。
