From the Department of Surgery (Ayed), from the Department of Pathology (Sohail, Rizvi), College of Medicine, University of Bisha; and from the Department of Urology (Alwadai), King Abdullah Hospital, Ministry of Health, Bisha, Kingdom of Saudi Arabia.
Saudi Med J. 2024 May;45(5):537-540. doi: 10.15537/smj.2024.45.5.20231019.
Renal lymphangiectasia (RL) is a rare condition in which lymphatic vessels are dilated giving rise to cyst formation in peripelvic, perirenal and intrarenal locations. Knowledge about RL is limited and based upon individual case reports. This can be genetic or acquired. There is no significant association with any gender or age. It can be manifested as focal or diffuse forms and can be unilateral or bilateral. Most of the cases present with abdominal or flank pain. The diagnosis is based on radiological imaging. Due to rarity of diseases, it has potential to be misdiagnosed as other cystic disease of kidneys. The treatment is mainly conservative but prolonged follow up for associated complications like hypertension and renal vein thrombosis is required. We have presented a case of bilateral renal lymphangiectasia with the review of available literature.
肾淋巴管扩张症（RL）是一种罕见的疾病，其特征为淋巴管扩张，导致肾盂周围、肾周和肾内出现囊状结构。目前对 RL 的了解有限，主要基于个案报道。RL 可分为遗传性和获得性，与任何性别或年龄均无明显关联。RL 可表现为局灶性或弥漫性，可为单侧或双侧。大多数病例表现为腹痛或腰痛。该病的诊断基于影像学检查。由于疾病罕见，RL 可能被误诊为其他肾脏囊性疾病。RL 的治疗主要为保守治疗，但需要长期随访以监测相关并发症，如高血压和肾静脉血栓形成。我们报告了一例双侧肾淋巴管扩张症，并对现有文献进行了回顾。
