Orouji Jokar Tahereh, Chidobem Ikechukwu, Khan Nazia
Hematology and Oncology, Prime Healthcare, Saint Clare's Hospital, Denville, USA.
Internal Medicine, Prime Healthcare, Saint Clare's Hospital, Denville, USA.
Cureus. 2021 Jul 3;13(7):e16130. doi: 10.7759/cureus.16130. eCollection 2021 Jul.
Renal lymphangiectasia is a rare benign mesenchymal tumor of unclear etiology resulting from dilatation of perinephric lymphatic channels and formation of cystic masses. Polycythemia is a rarely associated finding with only five cases reported in the literature. We report a case of bilateral renal lymphangiectasia associated with polycythemia in a 38-year-old man who was managed conservatively with pain control. There are no clear guidelines for the management of renal lymphangiectasia; although most patients can be treated conservatively, some cases, whose diagnosis is unclear or develop complications, require definitive surgical excision.
肾淋巴管扩张症是一种病因不明的罕见良性间充质肿瘤,由肾周淋巴管扩张和囊性肿块形成引起。红细胞增多症是一种罕见的相关表现,文献中仅报道了5例。我们报告一例38岁男性双侧肾淋巴管扩张症合并红细胞增多症,该患者通过控制疼痛进行保守治疗。目前对于肾淋巴管扩张症的治疗尚无明确指南;尽管大多数患者可采用保守治疗,但一些诊断不明确或出现并发症的病例需要进行确定性手术切除。