Yaynishet Yodit Abraham, Abera Michael Teklehaimanot, Reta Birhanu Kassie, Dojamo Demelash Darota, Abrar Fadil Nuredin, Legesse Tesfaye Kebede, Dessie Tesfahun Amsal
Addis Ababa University, College of Health Sciences, Department of Radiology, Addis Ababa, Ethiopia.
Addis Ababa University, College of Health Sciences, Department of Pathology, Addis Ababa, Ethiopia.
Radiol Case Rep. 2024 May 11;19(8):3130-3135. doi: 10.1016/j.radcr.2024.04.053. eCollection 2024 Aug.
Castleman's disease is a rare benign lymphangioproliferative disorder. The hyaline vascular subtype has a better outcome and is curable after surgical resection. Typically, Castleman disease manifests in the thorax, with rare reports of a renal hilum location. We present a 42-year-old male patient who had an incidentally detected right hilar hyaline vascular type of Castleman's disease, which we managed with surgical excision. Cross-sectional imaging modalities help in suggesting the diagnosis based on enhancement patterns and, more importantly, define the extent of the tumor pre-operatively. Although the renal hilum is a rare location for Castleman disease, it needs to be considered when imaging features suggest it.
卡斯特leman病是一种罕见的良性淋巴管增生性疾病。透明血管亚型预后较好,手术切除后可治愈。通常,卡斯特leman病表现在胸部,肾门部位的报道罕见。我们报告一例42岁男性患者,偶然发现右肾门透明血管型卡斯特leman病,我们对其进行了手术切除。横断面成像方式有助于根据强化模式提示诊断,更重要的是,在术前明确肿瘤范围。虽然肾门是卡斯特leman病的罕见部位,但当影像学特征提示时需要考虑。