Gaudioso Piergiorgio, Biancoli Elia, Battistuzzi Veronica, Concheri Stefano, Saccardo Tommaso, Franchella Sebastiano, Contro Giacomo, Taboni Stefano, Zanoletti Elisabetta, Causin Francesco, Nico Lorena, Gabrieli Joseph Domenico, Maroldi Roberto, Nicolai Piero, Ferrari Marco
Section of Otorhinolaryngology-Head and Neck Surgery, Department of Neurosciences, "Azienda Ospedale Università di Padova", University of Padua, 35128 Padua, Italy.
Unit of Otorhinolaryngology-Head and Neck Surgery, Azienda Ospedale Università Padova, 35128 Padua, Italy.
J Pers Med. 2024 Apr 28;14(5):465. doi: 10.3390/jpm14050465.
Spontaneous orbital cephaloceles are a rare condition. The purpose of this study is to provide a description of a clinical case and to carry out a systematic literature review.
A systematic review of the English literature published on the Pubmed, Scopus, and Web of Science databases was conducted, according to the PRISMA recommendations.
A 6-year-old patient was admitted for right otomastoiditis and thrombosis of the sigmoid and transverse sinuses, as well as the proximal portion of the internal jugular vein. Radiological examinations revealed a left orbital mass (22 × 14 mm) compatible with asymptomatic orbital meningocele (MC) herniated from the superior orbital fissure (SOF). The child underwent a right mastoidectomy. After the development of symptoms and signs of intracranial hypertension (ICH), endovascular thrombectomy and transverse sinus stenting were performed, with improvement of the clinical conditions and reduction of the orbital MC. The systematic literature review encompassed 29 publications on 43 patients with spontaneous orbital MC. In the majority of cases, surgery was the preferred treatment.
The present case report and systematic review highlight the importance of ICH investigation and a pathophysiological-oriented treatment approach. The experiences described in the literature are limited, making the collection of additional data paramount.
自发性眶部脑膨出是一种罕见疾病。本研究旨在描述一例临床病例并进行系统的文献综述。
根据PRISMA建议，对在PubMed、Scopus和Web of Science数据库上发表的英文文献进行系统综述。
一名6岁患者因右耳乳突炎、乙状窦和横窦血栓形成以及颈内静脉近端血栓形成入院。影像学检查发现左侧眼眶有一肿块（22×14毫米），符合从上眼眶裂（SOF）疝出的无症状眼眶脑膜膨出（MC）。该患儿接受了右乳突切除术。在出现颅内高压（ICH）的症状和体征后，进行了血管内血栓切除术和横窦支架置入术，临床状况得到改善，眼眶MC缩小。系统文献综述涵盖了29篇关于43例自发性眼眶MC患者的出版物。在大多数情况下，手术是首选治疗方法。
本病例报告和系统综述强调了ICH检查和以病理生理为导向的治疗方法的重要性。文献中描述的经验有限，因此收集更多数据至关重要。
