Magdoud Khaoula, Abouda Hassine Saber, Jellouli Asma, Ben Hmid Rim, Chanoufi Mohamed Badis, Karoui Abir
Maternity and neonatology centre of Tunis, Emergency department.
University of Tunis el Manar, Faculty of Medicine of Tunis, Tunis, Tunisia.
Tunis Med. 2024 May 5;102(5):310-314. doi: 10.62438/tunismed.v102i5.4738.
Rokitansky syndrome or Mayer Rokitansky Kuster Hauser (SRKMH) is a rare congenital malformation defined by uterovaginal aplasia. The aim of the treatment is to create a neovagina and restore sexual life. However, postoperative results in terms of sexual and overall quality of life of patients remain controversial.
To evaluate the quality of life and sexuality of patients operated on for Rokitansky syndrome.
This was a retrospective and comparative study between two groups of patients. The first group consisted of patients who had undergone vaginoplasty as part of SRKMH. The second group was that of the controls. Control in terms of sexual function by the Ar FSFI (Arab FemaleSexualFunction Index) and quality of life by the SF36 (Short Forms Health Survey) were used in both groups.
The average age of patients operated on for SRKMH was 22.53 years. Eighteen of these patients (60%) were sexually active at the time of the study. Patients operated on for SRKMH had a significantly lower Ar FSFI score compared to the control group. The two areas most affected were lubrication and pain. Likewise, patients who underwent vaginoplasty had a significantly lower SF 36 score compared to the control group. The psychological component was the most affected of the different components of quality of life.
Sexual function and quality of life after vaginoplasty in the context of Rokitansky syndrome remains unsatisfactory despite the anatomical result.
罗基坦斯基综合征或梅耶-罗基坦斯基-库斯特-豪泽综合征（SRKMH）是一种以子宫阴道发育不全为特征的罕见先天性畸形。治疗的目的是创建一个新阴道并恢复性生活。然而，术后患者的性功能和整体生活质量的结果仍存在争议。
评估接受罗基坦斯基综合征手术治疗患者的生活质量和性功能。
这是一项两组患者之间的回顾性比较研究。第一组由接受阴道成形术作为SRKMH治疗一部分的患者组成。第二组为对照组。两组均采用阿拉伯女性性功能指数（Ar FSFI）评估性功能，采用简短健康调查问卷（SF36）评估生活质量。
接受SRKMH手术治疗的患者平均年龄为22.53岁。其中18名患者（60%）在研究时具有性活动能力。与对照组相比，接受SRKMH手术治疗的患者Ar FSFI评分显著更低。受影响最大的两个方面是润滑和疼痛。同样，与对照组相比，接受阴道成形术的患者SF 36评分显著更低。生活质量的不同组成部分中，心理成分受影响最大。
尽管解剖学结果良好，但在罗基坦斯基综合征背景下，阴道成形术后的性功能和生活质量仍不尽人意。
