Vitols Jurgis, Lidaka Lasma
JV Clinic SIA "Vītols and Vītols", Raiskuma iela 1, Riga LV-1006, Latvia.
Department of Paediatric Gynaecology Children's Clinical University Hospital, Vienibas gatve 45, Riga LV-1004, Latvia.
Case Rep Obstet Gynecol. 2024 Jun 8;2024:9498667. doi: 10.1155/2024/9498667. eCollection 2024.
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is a female congenital disorder characterized by an underdeveloped or absent vagina and uterus. The first-line treatment to create a neovagina is patient-performed vaginal dilatation. We report here the rare case of an MRKH patient who presented with urethral dilatation and was successfully treated with Davydov vaginoplasty. Seventeen-year-old patient with known single kidney was consulted by a gynaecologist, and a diagnosis of MRKH syndrome was established. As the patient had urethral dilatation-resulting from repetitive intraurethral intercourse-neovaginal creation by means of self-performed vaginal dilatation was precluded. Rather, the Davydov vaginoplasty was successfully performed; there were no postoperative complications, and the patient was fully continent postsurgery. MRKH patients and healthcare providers should be educated on the damaging consequences of intraurethral intercourse. More cases need to be reported to establish the best treatment options for a normal sexual life.
梅耶-罗基坦斯基-库斯特-豪泽（MRKH）综合征是一种女性先天性疾病，其特征为阴道和子宫发育不全或缺失。创建新阴道的一线治疗方法是患者自行进行阴道扩张。我们在此报告一例罕见的MRKH患者，该患者出现尿道扩张，并通过达维多夫阴道成形术成功治愈。一名17岁已知单肾的患者由妇科医生会诊，确诊为MRKH综合征。由于该患者因反复尿道内性交导致尿道扩张，因此无法通过自行进行阴道扩张来创建新阴道。相反，成功实施了达维多夫阴道成形术；术后无并发症，患者术后完全控尿。应向MRKH患者和医疗服务提供者宣传尿道内性交的有害后果。需要报告更多病例，以确定实现正常性生活的最佳治疗方案。
