Department of Nephrology, Akanksha Hospital, Lambhvel, Anand, Gujarat, India.
Department of Critical Care Medicine, Akanksha Hospital, Lambhvel, Anand, Gujarat, India.
Saudi J Kidney Dis Transpl. 2023 Sep 1;34(5):455-457. doi: 10.4103/1319-2442.397208. Epub 2024 Mar 11.
Distal renal tubular acidosis (dRTA), also known as Type 1 renal tubular acidosis, is a rare disorder. It primarily occurs through the inability to secrete H+ ions. The causes of dRTA can be divided into primary and secondary. The most common secondary cause of dRTA is Sjögren syndrome. dRTA typically presents as hypokalemia with non-anion gap metabolic acidosis. Here, we present a patient where Sjögren's syndrome causing dRTA was masked by the presence of hypernatremia causing metabolic acidosis with a high anion gap.
远端肾小管性酸中毒（dRTA），又称 1 型肾小管性酸中毒，是一种罕见的疾病。它主要是由于不能分泌 H+离子而引起的。dRTA 的病因可分为原发性和继发性。dRTA 最常见的继发性病因是干燥综合征。dRTA 通常表现为低钾血症伴非阴离子间隙性代谢性酸中毒。在这里，我们介绍了一例由干燥综合征引起的 dRTA 患者，由于高钠血症导致代谢性酸中毒伴高阴离子间隙而掩盖了 dRTA。
