原发性干燥综合征伴远端肾小管酸中毒和横纹肌溶解症。
Primary Sjö-gren's syndrome presenting with distal, renal tubular acidosis and rhabdomyolysis.
作者信息
Prakash E B S, Fernando M E, Sathiyasekaran Malathi, Bhoopathy R M, Jayanth J J, Samuel J
机构信息
CSI Kalyani Multispeciality Hospital, 15, Dr. Radhakrishnan Salai, Mylapore, Chennai.
出版信息
J Assoc Physicians India. 2006 Dec;54:949-50.
Primary Sjögren's syndrome (PSS) is rare in India. Clinically manifest renal disease in PSS is uncommon and is usually an autoimmune tubulointerstitial nephritis presenting with distal renal tubular acidosis (dRTA) or a urinary concentrating defect. Hypokalemic paralysis due to dRTA in PSS is rare but well documented in medical literature. Rhabdomyolysis as a consequence of hypokalemia in PSS is exceptional. We report a case of PSS with dRTA and rhabdomyolysis causing prolonged respiratory failure and quadriparesis.
原发性干燥综合征（PSS）在印度较为罕见。PSS临床上出现肾脏疾病并不常见，通常是一种自身免疫性肾小管间质性肾炎，表现为远端肾小管酸中毒（dRTA）或尿浓缩功能缺陷。PSS中由dRTA导致的低钾性麻痹很少见，但在医学文献中有充分记载。PSS中因低钾血症导致横纹肌溶解则极为罕见。我们报告一例患有dRTA和横纹肌溶解的PSS病例，该病例导致了长时间的呼吸衰竭和四肢瘫痪。
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