Moon Yijun, Kim Haneul, Park Hojin
Department of Plastic and Reconstructive Surgery, Korea University Anam Hospital, Korea University College of Medicine, Seoul, Korea.
Arch Craniofac Surg. 2024 Aug;25(4):192-196. doi: 10.7181/acfs.2023.00598. Epub 2024 Jul 17.
Angiolymphoid hyperplasia with eosinophilia (ALHE) is a rare condition characterized by nodular lesions predominantly in the head and neck region, often causing discomfort or pain. Treatment remains challenging because of its rarity and the lack of established guidelines. This report presents a case of ALHE affecting the earlobes that was successfully managed using ear lobule reduction surgery and subsequent intralesional steroid injections. A 31-year-old woman with a history of recurrent earlobe masses underwent a partial excision to avoid the loss of the earlobe. Histopathological examination confirmed Kimura disease, a variant of ALHE. Subsequent local methylprednisolone injections effectively controlled the remaining lesions, resulting in significant size reduction without notching. Various treatment modalities have been attempted for this condition; however, recurrence rates remain high. Surgical resection combined with intralesional corticosteroid injections is the preferred approach. In this case, a sub-antitragal groove technique for earlobe reduction was employed to preserve the lateral edge of the ear lobule, minimize the risk of deformity, and achieve a predictable outcome. The sub-antitragal groove technique offers an approach to reduce earlobe size without compromising aesthetics. Further research is required to elucidate the pathogenesis of ALHE and establish standardized treatment protocols for this rare condition.
嗜酸性粒细胞增多性血管淋巴样增生(ALHE)是一种罕见疾病,其特征为主要位于头颈部的结节性病变,常引起不适或疼痛。由于其罕见性以及缺乏既定的指南,治疗仍然具有挑战性。本报告介绍了一例累及耳垂的ALHE病例,该病例通过耳垂缩小手术及随后的病损内类固醇注射成功得到治疗。一名有复发性耳垂肿物病史的31岁女性接受了部分切除术以避免耳垂缺失。组织病理学检查确诊为木村病,这是ALHE的一种变体。随后的局部甲基强的松龙注射有效控制了剩余病变,使病变大小显著缩小且无切迹。针对这种疾病已尝试了多种治疗方式;然而,复发率仍然很高。手术切除联合病损内皮质类固醇注射是首选方法。在本病例中,采用了一种耳屏前沟技术进行耳垂缩小,以保留耳垂的外侧边缘,将畸形风险降至最低,并获得可预测的结果。耳屏前沟技术提供了一种在不影响美观的情况下缩小耳垂大小的方法。需要进一步研究以阐明ALHE的发病机制,并为这种罕见疾病建立标准化的治疗方案。