Gohri Jay, Luthra Harshvardhan, Qureshi Khushboo, Reddy Karnati Prudhveer
Department of Medicine, JSS Medical College and Hospital, Mysore, Karnataka, India.
Department of Cardiology, Vinnitsa National Medical University named after M.I.Pirogov, Danyla Hoholytska 58a, Vinnytsia Oblast, 21036, Ukraine.
Cardiooncology. 2024 Aug 8;10(1):49. doi: 10.1186/s40959-024-00251-z.
Cardiac sarcoidosis though in itself, a rare entity, very rarely presents primarily with conduction abnormalities as the primary manifestation in the spectrum of presentations accounted by this chronic granulomatous systemic disease. Sarcoidosis presenting as intra-atrial masses is virtually unheard of.
A middle aged female presented with progressive conduction system disease was found to have right atrial masses of unclear etiologic on relevant imaging. Over the course of 3 months she underwent a dual-chamber ICD implant for her eventual complete heart block and a surgical resection following an inconclusive biopsy of the right atrial free wall mass. She was then diagnosed with cardiac sarcoidosis and started on immunosupressants almost instantaneously as a part of her treatment.
This is an entirely new and unreported presentation of cardiac sarcoidosis as an intra-atrial mass. Through this case we bring light to cardiac sarcoidosis as a potential differential for intra-cardiac masses and how with available data do we go about treating it.
心脏结节病本身是一种罕见疾病，在这种慢性肉芽肿性全身性疾病的各种表现中，以传导异常为主要表现的情况极为罕见。以心房内肿块形式出现的结节病几乎闻所未闻。
一名中年女性因进行性传导系统疾病就诊，相关影像学检查发现其右心房有病因不明的肿块。在3个月的病程中，她因最终出现完全性心脏传导阻滞接受了双腔植入式心脏复律除颤器植入术，并在右心房游离壁肿块活检结果不明确后接受了手术切除。随后她被诊断为心脏结节病，并几乎立即开始使用免疫抑制剂作为治疗的一部分。
这是心脏结节病以心房内肿块形式出现的一种全新且未报道过的表现。通过这个病例，我们揭示了心脏结节病作为心内肿块的一种潜在鉴别诊断，以及根据现有数据我们应如何对其进行治疗。
