Hu Chenhao, Gao Fengxiang, Zhang Ying, Guo Bin
Department of Otolaryngology,Qinghai University Affiliated Hospital,Xining,810001,China.
Lin Chuang Er Bi Yan Hou Tou Jing Wai Ke Za Zhi. 2024 Aug;38(8):755-757. doi: 10.13201/j.issn.2096-7993.2024.08.016.
Rosai Dorfman disease is a rare non Langerhans histiocytic disease with intranodal and/or extranodal manifestations, most commonly affecting cervical lymph nodes. There is no treatment guideline for this disease. This paper reports a case of infraglottic portion, which did not show typical symptoms, such as fever or lymphadenopathy, and was easily misdiagnosed as malignant tumor preoperatively. The patient underwent low-temperature plasma minimally invasive surgery combined with hormone therapy and achieved good clinical effect. By reviewing the literature, we can better understand the clinical manifestations, diagnosis and treatment of this rare disease.
罗萨伊-多夫曼病是一种罕见的非朗格汉斯组织细胞增多症,有淋巴结内和/或淋巴结外表现,最常累及颈部淋巴结。目前尚无针对该疾病的治疗指南。本文报道了1例声门下型病例,该病例未表现出如发热或淋巴结病等典型症状,术前易被误诊为恶性肿瘤。该患者接受了低温等离子体微创手术联合激素治疗,取得了良好的临床效果。通过文献复习,我们可以更好地了解这种罕见疾病的临床表现、诊断和治疗。