Zahid Khan Tariq, Bashir Afeera, Javeria Malik, Mehfooz Sana, Ahmed Zeba, Raja Sandesh, Ali Azzam, Raja Adarsh, Khanal Anuva
Department of ENT-Head & Neck Surgery, Dr. Ruth K. M. Pfau, Civil Hospital.
Dow Medical College, Dow University of Health Sciences.
Ann Med Surg (Lond). 2024 Apr 11;86(8):4758-4761. doi: 10.1097/MS9.0000000000002031. eCollection 2024 Aug.
Angioleiomyoma, a benign tumour of the smooth muscles of blood vessels, primarily affects individuals aged 30-50 years, with a higher incidence in females. While it commonly affects the lower extremities, it can also develop in the head and neck. However, hypopharyngeal angioleiomyomas are extremely rare, with only one documented case in world literature.
The authors present a rare case of a 70-year-old male with symptoms of voice change and deglutition discomfort. Imaging studies indicated a hypopharyngeal mass. Direct laryngoscopy showed a well-defined mass originating from the left lateral pharyngeal wall, obstructing the left vallecula and pyriform sinus. The patient underwent anterolateral pharyngotomy with mass excision.
After a successful anterolateral pharyngotomy, the patient experienced significant improvement in symptoms.
Diagnosing and managing hypopharyngeal angioleiomyoma is challenging due to its unusual location. Its rarity emphasizes the importance of considering it as a possible differential when evaluating hypopharyngeal masses.
血管平滑肌瘤是一种血管平滑肌的良性肿瘤,主要影响30至50岁的人群,女性发病率更高。虽然它通常影响下肢,但也可发生于头颈部。然而,下咽血管平滑肌瘤极为罕见,世界文献中仅有一例记载。
作者报告了一例罕见病例,一名70岁男性出现声音改变和吞咽不适症状。影像学检查显示下咽有肿物。直接喉镜检查发现一个边界清晰的肿物,起源于左侧咽侧壁,阻塞了左侧梨状窝和会厌谷。患者接受了前外侧咽切开术并切除肿物。
前外侧咽切开术成功后,患者症状明显改善。
由于下咽血管平滑肌瘤位置特殊,诊断和治疗具有挑战性。其罕见性凸显了在评估下咽肿物时将其作为可能的鉴别诊断考虑的重要性。