Rogando Dillon, Patel Dhruv, Robles Jeffrey, Ranjbar Tara, Mukharjee Sourodip, Chan Debra H, Clarke Erika, Mukherjee Indraneil
General Surgery, City College of New York School of Medicine, New York, USA.
Surgery, City College of New York School of Medicine, New York, USA.
Cureus. 2024 Jul 14;16(7):e64514. doi: 10.7759/cureus.64514. eCollection 2024 Jul.
Median arcuate ligament syndrome (MALS) is a rare gastroenterological illness that arises from the compression of the celiac trunk by the fibrous arch known as the median arcuate ligament, which connects the muscular tendon of the diaphragm to the vertebral column. It is hypothesized that this syndrome arises due to the inadequate caudal migration of the celiac trunk during embryogenesis, although the exact pathophysiology behind this disease process remains unclear. While MALS is classically associated with a triad of post-prandial pain, weight loss, and epigastric bruit, the triad is often incomplete due to variations in vascular structures with collateral circulation from adjacent vessels. When symptoms are present, they can be vague and often characterized as unexplained nausea, vomiting, diarrhea, or flatulence. Frequently, MALS is identified incidentally upon imaging of the abdomen in response to these nonspecific complaints. We present the case of a patient suffering from MALS in which a rare anatomic variant of the celiac trunk was identified.
正中弓状韧带综合征(MALS)是一种罕见的胃肠疾病,由被称为正中弓状韧带的纤维弓压迫腹腔干引起,该韧带连接膈肌肌腱与脊柱。据推测,该综合征是由于胚胎发育过程中腹腔干尾侧迁移不足所致,尽管这一疾病过程的确切病理生理学仍不清楚。虽然MALS典型地与餐后疼痛、体重减轻和上腹部杂音三联征相关,但由于血管结构的变异以及来自相邻血管的侧支循环,三联征往往并不完整。当出现症状时,症状可能不明确,常表现为不明原因的恶心、呕吐、腹泻或肠胃胀气。通常,MALS是在对这些非特异性症状进行腹部成像时偶然发现的。我们报告了一例患有MALS的患者,该患者被发现存在一种罕见的腹腔干解剖变异。