Pandey Gaurav, Butt Salman, Aljassim Obaid M
Cardiothoracic Surgery, Dubai Hospital, Dubai, ARE.
Cardiac Surgery, Heart Vascular and Thoracic Institute, Cleveland Clinic Abu Dhabi, Abu Dhabi, ARE.
Cureus. 2024 Jul 19;16(7):e64892. doi: 10.7759/cureus.64892. eCollection 2024 Jul.
This case report documents a rare congenital anomaly in a 27-year-old man of African descent presenting with exertional chest discomfort and shortness of breath, diagnosed with a ruptured right sinus of Valsalva (RSOV) aneurysm dissecting into the interventricular septum (IVS), creating an aneurysmal cavity. Such occurrences are typically rare, with this type of aneurysm largely manifesting in the right atrium, making its presentation in the IVS without intracardiac communication exceptionally uncommon. Cardiac imaging, including transesophageal echocardiography and cardiac magnetic resonance imaging (CMR), played pivotal roles in visualizing the structural abnormality and planning the subsequent surgical intervention. The patient's treatment included heart failure optimization, followed by surgery to repair the aneurysmal cavity while preserving the native aortic valve. Postoperative challenges included a complete heart block managed by cardiac resynchronization therapy and an intracardiac defibrillator. The report underscores the importance of advanced imaging in diagnosing and managing rare cardiac anomalies, highlighting the aneurysm's unique rupture pattern and location.
本病例报告记录了一名27岁非洲裔男性的罕见先天性异常,该患者出现劳力性胸部不适和呼吸急促,被诊断为右冠状动脉窦(RSOV)动脉瘤破裂并累及室间隔(IVS),形成一个动脉瘤腔。这种情况通常很少见,这类动脉瘤大多出现在右心房,而其在无心脏内交通的室间隔出现极为罕见。心脏成像,包括经食管超声心动图和心脏磁共振成像(CMR),在可视化结构异常和规划后续手术干预方面发挥了关键作用。患者的治疗包括优化心力衰竭治疗,随后进行手术修复动脉瘤腔,同时保留原生主动脉瓣。术后挑战包括通过心脏再同步治疗处理的完全性心脏传导阻滞和植入心脏内除颤器。该报告强调了先进成像在诊断和管理罕见心脏异常中的重要性,突出了动脉瘤独特的破裂模式和位置。