Alizadehasl Azin, Hakimian Hoda, Dokhani Negar, Pouraliakbar Hamidreza, Firoozbakhsh Parisa
Cardio-Oncology Research Center, Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Rajaie Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
Radiol Case Rep. 2024 Jul 26;19(10):4308-4311. doi: 10.1016/j.radcr.2024.06.088. eCollection 2024 Oct.
Undifferentiated pleomorphic cardiac sarcomas are extremely rare, highly malignant mesenchymal cardiac neoplasms typically presenting in the sixth decade of life. Here, we have reported a rare case of undifferentiated pleomorphic cardiac sarcoma presenting with dyspnea in a young male. On further evaluations, a large, ill-defined, multilobulated mass was observed in left atrium (LA) with encasement of left circumflex artery, attachment to mitral valve annulus, and invasion through LA wall and pericardium.
未分化多形性心脏肉瘤极为罕见,是一种高度恶性的间质性心脏肿瘤,通常在60岁左右出现。在此,我们报告了一例罕见的未分化多形性心脏肉瘤,该病例为一名年轻男性,表现为呼吸困难。进一步评估发现,左心房(LA)有一个大的、边界不清的多叶状肿块,包绕左旋支动脉,附着于二尖瓣环,并侵及左心房壁和心包。