Almalki Wafa, Alzahrani Majdi, Alssaqqaf Ihab, Baker Bilal
College of Medicine, Umm Alqura University, Al ABadia Rd, 24243 Makkah, Saudi Arabia.
King Abdullah Medical City, 21955, Muzdalifah Rd, Makkah, Saudi Arabia.
Int J Surg Case Rep. 2021 Dec;89:106555. doi: 10.1016/j.ijscr.2021.106555. Epub 2021 Nov 2.
Undifferentiated pleomorphic sarcoma (UPS) is one of the most common sarcomas affecting elderly patients, majority of UPS usually in the extremities, trunk, and retroperitoneum. However, its rarely observed in the digestive system. There are minimal data published regarding this topic.
Here we present a 58 years old female patient with a rare case of the pleomorphic sarcoma of retro-gastric mass measures about (24.7 × 23.5 × 17.4 cm) who underwent exploration laparotomy founded a freely and mobile retro-gastric mass measuring 30 × 20 cm with a cystic and solid component. The mass was freely and mobile located with no true gastric relation is the first one to be reported.
The undifferentiated pleomorphic sarcomas or MFH has been regarded as the most common soft tissue sarcoma for many years (Kabashima et al., 2017). The incidence increases with age, with an inclusive incidence of about 1-2 cases per 100,000 patients per year, predominately 1.2:1 for males. Undifferentiated pleomorphic sarcoma of the stomach is rare and counted to have a worse prognosis when compared to the other types of pleomorphic malignant fibrous histiocytoma.
We present a rare case of high-grade undifferentiated pleomorphic sarcoma of the retro-gastric mass with no invasion to the surrounding structures, managed with surgical resection of the tumor.
未分化多形性肉瘤(UPS)是影响老年患者的最常见肉瘤之一,大多数UPS通常发生在四肢、躯干和腹膜后。然而,在消化系统中很少见。关于这个主题发表的数据极少。
我们在此呈现一名58岁女性患者,患有罕见的胃后肿块多形性肉瘤,肿块大小约为(24.7×23.5×17.4厘米),接受剖腹探查时发现一个大小为30×20厘米、可自由移动的胃后肿块,有囊性和实性成分。该肿块可自由移动,与胃无真正关联,这是首例报告。
多年来,未分化多形性肉瘤或恶性纤维组织细胞瘤一直被认为是最常见的软组织肉瘤(Kabashima等人,2017年)。发病率随年龄增长而增加,每年每10万名患者中约有1 - 2例,男性与女性的发病率之比主要为1.2:1。胃未分化多形性肉瘤罕见,与其他类型的多形性恶性纤维组织细胞瘤相比,预后较差。
我们报告了一例罕见的胃后肿块高级别未分化多形性肉瘤,未侵犯周围结构,通过手术切除肿瘤进行治疗。