Sharma Anjali, Vyas Praveena, Agarwal Deshant
Department of Pathology, Bhagwan Mahaveer Cancer Hospital and Research Center, Jaipur, Rajasthan, India.
J Oral Maxillofac Pathol. 2023 Feb;27(Suppl 1):S33-S37. doi: 10.4103/jomfp.jomfp_107_21. Epub 2023 Feb 4.
Undifferentiated pleomorphic sarcoma (UPS) previously called as malignant fibrous histiocytoma comprises a group of high-grade pleomorphic sarcomas that cannot be otherwise classified and considered as a diagnosis of exclusion. In the head neck region, UPS is extremely rare and accounts for 3% of all the undifferentiated pleomorphic sarcomas. Some of the reported sites include maxilla, mandible, buccal mucosa, temperomandibular fossa, tongue, gingiva, paranasal sinuses, salivary glands, and retro-orbital soft tissue. Undifferentiated pleomorphic sarcoma of the floor of the mouth is very rare. To our knowledge, only one case has been reported earlier. We report the second case of undifferentiated pleomorphic sarcoma of the floor of mouth.
未分化多形性肉瘤(UPS)以前称为恶性纤维组织细胞瘤,是一组无法进行其他分类的高级别多形性肉瘤,被视为排除性诊断。在头颈部区域,UPS极为罕见,占所有未分化多形性肉瘤的3%。一些报道的发病部位包括上颌骨、下颌骨、颊黏膜、颞下颌窝、舌、牙龈、鼻窦、唾液腺和眶后软组织。口底未分化多形性肉瘤非常罕见。据我们所知,此前仅报道过1例。我们报告第2例口底未分化多形性肉瘤。