Inam Rida, Mehmood Asim, Mahmood Attia, Badshah Maaz B, Shafiq Usama
Internal Medicine, Shifa College of Medicine, Islamabad, PAK.
Medicine, Ayub Teaching Hospital, Abbottabad, PAK.
Cureus. 2024 Jul 22;16(7):e65118. doi: 10.7759/cureus.65118. eCollection 2024 Jul.
We report an interesting case of a 25-year-old male patient who presented with a complaint of pain in the abdomen for six months, which was not associated with any other symptom, the patient was diagnosed with IgG4-related retroperitoneal fibrosis (RF) via endoscopic ultrasound (EUS)-guided biopsy. He was prescribed steroids and proton pump inhibitors. Due to the limited presentation and rarity of RF, diagnosis of this disease requires extensive diligence and care. In this case report, we underscore the importance of considering the differential diagnosis of RF or Ormond's disease when a patient presents with vague symptoms of pain in the abdomen. According to our knowledge, this is the first case of IgG4-related RF in a patient with B-cell lymphoproliferative disorder reported from Pakistan.
我们报告了一例有趣的病例，一名25岁男性患者主诉腹部疼痛6个月，无任何其他伴随症状，经内镜超声（EUS）引导下活检诊断为IgG4相关性腹膜后纤维化（RF）。他接受了类固醇和质子泵抑制剂治疗。由于RF临床表现有限且罕见，对该疾病的诊断需要高度的谨慎和关注。在本病例报告中，我们强调当患者出现腹部隐痛等模糊症状时，考虑RF或奥蒙德病鉴别诊断的重要性。据我们所知，这是巴基斯坦报道的首例患有B细胞淋巴增殖性疾病的患者发生IgG4相关性RF的病例。
