Department of Pediatric Cardiology, Pamukkale University Medical School, Denizli, Türkiye.
Department of Nuclear Medicine, Pamukkale University Medical School, Denizli, Türkiye.
Turk Kardiyol Dern Ars. 2024 Sep;52(6):460-463. doi: 10.5543/tkda.2023.59829.
Swyer-James-MacLeod syndrome is characterized radiologically by hyperlucency in a single lung lobe, accompanied by reduced vascularity, alveolar hyperdistention, and air trapping, without bronchial airway obstruction. The most common congenital heart defect in childhood, ventricular septal defect, leads to irreversible pulmonary hypertension and Eisenmenger syndrome if not treated promptly. This case report presents a 25-year-old patient with Swyer-James-MacLeod syndrome and Eisenmenger syndrome. It is crucial to include Swyer-James-MacLeod syndrome in the differential diagnosis of patients with atypically distributed pulmonary emphysema and unilateral hyperlucency for early diagnosis and timely intervention.
斯韦尔-詹姆斯-麦克劳德综合征的影像学特征为单一肺叶透亮度过高，伴有肺血管减少、肺泡过度膨胀和空气滞留，但无支气管气道阻塞。室间隔缺损是儿童期最常见的先天性心脏病，如果不及时治疗，会导致不可逆转的肺动脉高压和艾森曼格综合征。本病例报告介绍了一例 25 岁的斯韦尔-詹姆斯-麦克劳德综合征合并艾森曼格综合征患者。在诊断非典型分布性肺气肿和单侧肺透亮度过高的患者时，将斯韦尔-詹姆斯-麦克劳德综合征纳入鉴别诊断非常重要，以便早期诊断和及时干预。
