Cardiovascular Medical Center, Kaohsiung Veterans General Hospital, Kaohsiung, Taiwan.
Division of Cardiology, Department of Medicine, Taipei Veterans General Hospital, Taipei, Taiwan.
Future Cardiol. 2024;20(11-12):605-611. doi: 10.1080/14796678.2024.2400855. Epub 2024 Sep 13.
The quadricuspid aortic valve (QAV) is a rare congenital anomaly. We report a 51-year-old woman with QAV who experienced intermittent chest pain due to fibrotic tissue overgrowth from the small left coronary cusp, obstructing the left main coronary artery (LM). Angiography revealed a large "Vieussens' arterial ring," which acted as a collateral channel from the right coronary artery to the left coronary artery, preserving coronary blood flow and left ventricular function. Surgery successfully removed the tissue, maintaining both aortic valve function and coronary patency. This case highlights the need to consider QAV complications and use various imaging modalities for accurate diagnosis and treatment planning, including evaluating potential issues like aortic regurgitation and coronary anomalies.
四叶式主动脉瓣(QAV)是一种罕见的先天性异常。我们报告了一例 51 岁女性 QAV 患者,因小左冠状动脉瓣的纤维组织过度生长而导致间歇性胸痛,从而阻塞了左主干冠状动脉(LM)。血管造影显示出一个大的“Vieussens 动脉环”,它充当了从右冠状动脉到左冠状动脉的侧支通道,维持了冠状动脉血流和左心室功能。手术成功地切除了组织,同时保留了主动脉瓣功能和冠状动脉通畅。本病例强调了需要考虑 QAV 并发症,并使用各种成像方式进行准确的诊断和治疗计划,包括评估潜在的主动脉瓣反流和冠状动脉异常等问题。