Mangerel Joshua, Masri Daniel, Gelbman Marshall
Department of Radiology, Maimonides Medical Center, 4802 10th Avenue, Brooklyn, NY 11219, USA.
Radiol Case Rep. 2024 Sep 6;19(12):5565-5568. doi: 10.1016/j.radcr.2024.08.078. eCollection 2024 Dec.
Pneumocephalus, is a general term describing the presence of air within the intracranial structures. It most commonly occurs due to dural injury, often the sequela of head trauma or surgery. More infrequently, nontraumatic pneumocephalus can be related to infection, Valsalva, fistulization between air-containing organs and intracranial structures, or vascular air embolism. While postsurgical pneumocephalus is often benign, serious consequences of pneumocephalus exist, including tension pneumocephalus and cerebral infarction. We present a case of air embolism and cerebral infarction in a patient with Ehlers-Danlos syndrome, found to have large cavitary lesion in the left upper lobe of the lung, with associated pulmonary vascular malformation seen on bronchoscopy. To our knowledge this is the first reported case of air embolism associated with a pulmonary cavitary lesion and vascular malformation, in a patient with Ehlers-Danlos syndrome.
气颅是描述颅内结构内存在空气的一个通用术语。它最常见于硬脑膜损伤，通常是头部外伤或手术的后遗症。较少见的情况下，非创伤性气颅可能与感染、瓦尔萨尔瓦动作、含气器官与颅内结构之间的瘘管形成或血管空气栓塞有关。虽然术后气颅通常是良性的，但气颅也存在严重后果，包括张力性气颅和脑梗死。我们报告一例患有埃勒斯-当洛综合征的患者发生空气栓塞和脑梗死，该患者在左肺上叶发现有大的空洞性病变，支气管镜检查可见相关的肺血管畸形。据我们所知，这是首例报道的埃勒斯-当洛综合征患者发生与肺空洞性病变和血管畸形相关的空气栓塞病例。
