Molecular Cardiology Research Institute, Tufts Medical Center, Boston, MA, USA.
Mother Infant Research Institute, Tufts Medical Center, Boston, MA, USA.
FEBS Lett. 2024 Nov;598(21):2670-2682. doi: 10.1002/1873-3468.15020. Epub 2024 Sep 19.
Heart failure (HF) is highly prevalent. Mechanisms underlying HF remain incompletely understood. Splicing factors (SF), which control pre-mRNA alternative splicing, regulate cardiac structure and function. This study investigated regulation of the splicing factor heterogeneous nuclear ribonucleoprotein-L (hnRNPL) in the failing heart. hnRNPL protein increased in left ventricular tissue from mice with transaortic constriction-induced HF and from HF patients. In left ventricular tissue, hnRNPL was detected predominantly in nuclei. Knockdown of the hnRNPL homolog Smooth in Drosophila induced cardiomyopathy. Computational analysis of predicted mouse and human hnRNPL binding sites suggested hnRNPL-mediated alternative splicing of tropomyosin, which was confirmed in C2C12 myoblasts. These findings identify hnRNPL as a sensor of cardiac dysfunction and suggest that disturbances of hnRNPL affect alternative splicing in HF.
心力衰竭(HF)的发病率很高。HF 的潜在机制仍不完全清楚。剪接因子(SF)控制前体 mRNA 的可变剪接,调节心脏结构和功能。本研究探讨了剪接因子异质核核糖核蛋白-L(hnRNPL)在衰竭心脏中的调节作用。hnRNPL 蛋白在主动脉缩窄诱导的 HF 小鼠和 HF 患者的左心室组织中增加。在左心室组织中,hnRNPL 主要在核内检测到。在果蝇中敲低 hnRNPL 同源物 Smooth 可诱导心肌病。对预测的小鼠和人 hnRNPL 结合位点的计算分析表明 hnRNPL 介导原肌球蛋白的可变剪接,在 C2C12 成肌细胞中得到证实。这些发现将 hnRNPL 鉴定为心脏功能障碍的传感器,并表明 hnRNPL 紊乱会影响 HF 中的可变剪接。