Selva Kumaran Kabilen, Shamsudin Nurul Syamiza, Dalip Singh Harvinder Singh, Devesahayam Philip Rajan
Otolaryngology - Head and Neck Surgery, Hospital Raja Permaisuri Bainun, Ipoh, MYS.
Otolaryngology - Head and Neck Surgery, Hospital Tuanku Ja'afar, Seremban, MYS.
Cureus. 2024 Sep 1;16(9):e68357. doi: 10.7759/cureus.68357. eCollection 2024 Sep.
Adamantinomatous craniopharyngioma (ACP) is one of the two types of craniopharyngioma recognized by the World Health Organization (WHO), the other being papillary craniopharyngioma (PCP). These rare, benign tumours of the pituitary region are classified as Grade 1 central nervous system (CNS) tumours. ACP predominantly affects adolescents aged 5-15 years and adults over 50 years. It is usually located in the sellar and suprasellar regions. We present the case of an 18-year-old Malaysian female with a six-year history of persistent epistaxis and progressive nasal obstruction, an atypical presentation of ACP. This report highlights an entirely ectopic location of ACP in the sinonasal region. The tumour encompassed the left nasal cavity, the left anterior and posterior ethmoid sinuses, and the bilateral frontal sinuses. The unusual presentation of this tumour was detected with the aid of CT and MRI and confirmed by histopathological examination. In this case report, we discuss a rare presentation, an unusual location, and the strategies employed to overcome these challenges.
造釉细胞瘤型颅咽管瘤（ACP）是世界卫生组织（WHO）认可的两种颅咽管瘤类型之一，另一种是乳头型颅咽管瘤（PCP）。这些罕见的垂体区良性肿瘤被归类为1级中枢神经系统（CNS）肿瘤。ACP主要影响5至15岁的青少年和50岁以上的成年人。它通常位于鞍区和鞍上区。我们报告一例18岁马来西亚女性病例，有六年持续性鼻出血和进行性鼻塞病史，这是ACP的非典型表现。本报告强调了ACP在鼻窦区域完全异位的位置。肿瘤累及左侧鼻腔、左侧前后筛窦和双侧额窦。借助CT和MRI检测到该肿瘤的异常表现，并经组织病理学检查证实。在本病例报告中，我们讨论了一种罕见的表现、不寻常的位置以及为克服这些挑战所采用的策略。
