Kajin Filip, Meyerhoff Nina, Meller Sebastian, Carlson Regina, Tipold Andrea, Gutierrez-Quintana Rodrigo, Kaczmarska Adriana, Sanchez-Masian Daniel, Ives Edward, Brocal Josep, von Klopmann Thilo, Hauer Julia, Volk Holger Andreas
Department of Small Animal Medicine and Surgery, University of Veterinary Medicine, Hannover, Germany.
Clinic for Internal Diseases, Faculty of Veterinary Medicine, University of Zagreb, Zagreb, Croatia.
Front Vet Sci. 2024 Sep 20;11:1453698. doi: 10.3389/fvets.2024.1453698. eCollection 2024.
Idiopathic generalized tremor syndrome is a disorder characterized by an acute onset of full-body tremors, sometimes accompanied by vestibulo-cerebellar signs, that is responsive to treatment with corticosteroids. Although considered to have an overall good outcome, relapsing and persistent mild clinical signs have been described. So far, little is known about the etiopathology of this syndrome, but it is believed to have an immune-mediated origin. In human medicine, description of numerous autoantibodies involved in certain non-infectious neurologic disorders has revolutionized understanding of their pathophysiology, diagnosis and treatment. In this multicenter retrospective study, we aimed to describe the clinical signs, course, and outcome of dogs with idiopathic generalized tremor syndrome and correlate potential findings with the presence or absence of autoantibodies associated with autoimmune cerebellar syndromes in humans. Information regarding signalment, history, clinical signs, laboratory findings, diagnostic imaging and testing for regional infectious diseases was gathered and the remaining serum and CSF samples were then analyzed for neural antibodies against targets associated with autoimmune encephalitic diseases of humans. Thirty-three dogs were included, and screening for neural antibodies was performed in 30 of those dogs. The analysis showed an increased titer of mGluR1 antibodies in two dogs, GFAP and later in the course of disease mGluR1 antibodies in one dog and an increase in unspecific autoantibodies which could not be further classified in two dogs. Dogs with detectable neural autoantibodies always had cerebrospinal fluid abnormalities in the form of a pleocytosis, with or without increased protein concentration, and tended to present with hyperthermia, potentially indicating a more severe clinical form of idiopathic generalized tremor syndrome in these cases. In conclusion, idiopathic generalized tremor syndrome is proposed to be an immune-mediated disorder potentially mediated by neural autoantibodies in a subgroup of dogs.
特发性全身性震颤综合征是一种以全身震颤急性发作为特征的疾病,有时伴有前庭小脑体征,对皮质类固醇治疗有反应。尽管总体预后良好,但也有复发和持续存在轻度临床体征的报道。到目前为止,对该综合征的病因病理学知之甚少,但据信其起源于免疫介导。在人类医学中,对某些非感染性神经系统疾病中涉及的众多自身抗体的描述彻底改变了对其病理生理学、诊断和治疗的认识。在这项多中心回顾性研究中,我们旨在描述特发性全身性震颤综合征犬的临床体征、病程和预后,并将潜在发现与人类自身免疫性小脑综合征相关自身抗体的有无进行关联。收集了有关信号、病史、临床体征、实验室检查结果、诊断性影像学检查以及局部传染病检测的信息,然后对剩余的血清和脑脊液样本进行分析,以检测针对与人类自身免疫性脑疾病相关靶点的神经抗体。共纳入33只犬,其中30只犬进行了神经抗体筛查。分析显示,两只犬的mGluR1抗体滴度升高,一只犬在疾病后期出现GFAP和mGluR1抗体升高,两只犬出现无法进一步分类的非特异性自身抗体升高。检测到神经自身抗体的犬总是存在脑脊液异常,表现为细胞增多,蛋白质浓度可升高或不升高,并且往往伴有体温过高,这可能表明这些病例中特发性全身性震颤综合征的临床症状更为严重。总之,特发性全身性震颤综合征被认为是一种免疫介导的疾病,在一部分犬中可能由神经自身抗体介导。