Shukla Khilan, Taheri Touraj, Baghaie Hooman, Breik Omar
Maxillofacial Surgery Department, Royal Brisbane and Women's Hospital, Brisbane, Australia.
Griffith University, Gold Coast, Australia.
Indian J Otolaryngol Head Neck Surg. 2024 Oct;76(5):3956-3961. doi: 10.1007/s12070-024-04752-2. Epub 2024 Jun 6.
Epithelioid haemangioendothelioma (EHE) is a rare vascular tumour that primarily affects the liver, lungs and bone. It is very rarely described in the head and neck region, and is exceptionally uncommon within the submandibular region. We report a very rare case of EHE originating in a lymph node within the submandibular salivary gland of a 54-year-old female patient. The tumour was resected and the patient was regularly followed up, with no recurrence of disease at 24 months postoperatively. A review of existing literature, clinical and immunohistopathological features are discussed, which highlight the diagnostic dilemma, absence of consensus for management and appropriate surveillance method associated with EHE.
上皮样血管内皮瘤（EHE）是一种罕见的血管肿瘤，主要累及肝脏、肺和骨骼。头颈部区域很少有相关描述，在下颌下区域则极为罕见。我们报告了一例非常罕见的EHE病例，起源于一名54岁女性患者下颌下唾液腺内的淋巴结。肿瘤被切除，患者接受定期随访，术后24个月无疾病复发。本文回顾了现有文献，并讨论了其临床和免疫组化病理特征，这些特征凸显了与EHE相关的诊断困境、治疗缺乏共识以及合适的监测方法。
