Suppr超能文献

亚太地区泛发性脓疱型银屑病管理共识推荐意见

Asia-Pacific consensus recommendations on the management of generalized pustular psoriasis.

作者信息

Choon Siew Eng, Foley Peter Anthony, Asawanonda Pravit, Fujita Hideki, Jo Seong-Jin, Shi Yu-Ling, Theng Colin, Affandi Azura Mohd, Bang Chul Hwan, Frez Maria Lorna, Huei Huang Yu, Le Huu Doanh, Kim Tae-Gyun, Morita Akimichi, Oon Hazel H, Fernández-Peñas Pablo, Rajatanavin Natta, Robinson Suganthy, Selvarajah Latha, Tsai Tsen-Fang

机构信息

Clinical School Johor Bahru, Jeffrey Cheah School of Medicine & Health Sciences, Monash University, Johor Bahru, Malaysia.

The University of Melbourne, St Vincent's Hospital Melbourne, Fitrozy, Victoria, Australia.

出版信息

J Dermatol. 2024 Dec;51(12):1579-1595. doi: 10.1111/1346-8138.17471. Epub 2024 Oct 10.

Abstract

Generalized pustular psoriasis (GPP) is a rare, chronic, heterogeneous, and potentially life-threatening disease characterized by primary, sterile, and macroscopically visible pustules with or without systemic symptoms. There are ethnic differences in the genetic mutations associated with GPP that might affect the clinical manifestations and treatment responses. Currently, there is limited evidence from the patient population in the Asia-Pacific (APAC) region, resulting in a general paucity of information on the effective management of patients with GPP in this region. This modified Delphi panel study aimed to identify current evidence and gain advanced insights to facilitate the development of a regionally tailored APAC consensus on the management of GPP. A systematic literature review (SLR) was conducted to identify published literature and develop consensus statements on (i) definition and clinical course, (ii) diagnosis of GPP, (iii) treatment outcomes, goals, and monitoring measures, and (iv) optimal management strategies and clinical practices. Statements were rated by a panel of dermatologists in two rounds, with the threshold for consensus at ≥80% agreement. Twenty experts from the APAC region reached consensus on 106 statements that were developed based on the SLR and experts' collective expertise. The experts agreed that GPP is a rare, severe, and potentially life-threatening condition that is distinct from plaque psoriasis. This consensus emphasized the importance of a tailored treatment strategy taking into account the GPP flare severity and each patient's unique clinical circumstances. The experts reached consensus on the severity classification of GPP flares and recommended first-line and maintenance treatment options for adult GPP, childhood GPP, and GPP in pregnancy. These consensus outcomes have been synthesized into treatment algorithms to guide dermatologists in the APAC region in their clinical decision-making processes.

摘要

泛发性脓疱型银屑病(GPP)是一种罕见的、慢性的、异质性的且可能危及生命的疾病,其特征为原发性、无菌性且肉眼可见的脓疱,可伴有或不伴有全身症状。与GPP相关的基因突变存在种族差异,这可能会影响临床表现和治疗反应。目前,亚太(APAC)地区患者群体的证据有限,导致该地区关于GPP患者有效管理的信息普遍匮乏。这项改良的德尔菲专家小组研究旨在识别当前证据并获得深入见解,以促进制定针对GPP管理的亚太地区定制共识。进行了一项系统文献综述(SLR),以识别已发表的文献,并就以下方面制定共识声明:(i)定义和临床病程,(ii)GPP的诊断,(iii)治疗结果、目标和监测措施,以及(iv)最佳管理策略和临床实践。声明由一组皮肤科医生分两轮进行评分,共识阈值为≥80%的一致同意率。来自亚太地区的20位专家就基于SLR和专家集体专业知识制定的106项声明达成了共识。专家们一致认为,GPP是一种罕见、严重且可能危及生命的疾病,与斑块状银屑病不同。这一共识强调了根据GPP发作的严重程度和每位患者独特的临床情况制定个性化治疗策略的重要性。专家们就GPP发作的严重程度分类达成了共识,并推荐了成人GPP、儿童GPP和妊娠期GPP的一线治疗和维持治疗方案。这些共识结果已被整合到治疗算法中,以指导亚太地区的皮肤科医生在临床决策过程中做出决策。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ccc1/11624156/4e97cd61f00c/JDE-51-1579-g003.jpg

文献AI研究员

20分钟写一篇综述,助力文献阅读效率提升50倍。

立即体验

用中文搜PubMed

大模型驱动的PubMed中文搜索引擎

马上搜索

文档翻译

学术文献翻译模型,支持多种主流文档格式。

立即体验