Tahir Muhammad, Martin Ardenne, Madelaire Carlina, Herrera Guillermo A, Maltese Carl, Shackelford Rodney E
Pathology and Laboratory Medicine, University of South Alabama College of Medicine, Mobile, USA.
Pathology, University of South Alabama College of Medicine, Mobile, USA.
Cureus. 2024 Sep 11;16(9):e69191. doi: 10.7759/cureus.69191. eCollection 2024 Sep.
Primary pulmonary angiosarcomas are rare malignancies, with aggressive clinical behavior and poor prognosis. Here we present a case of a rare primary pulmonary epithelioid angiosarcoma in a 59-year-old woman who initially presented with right-sided chest pain and shortness of breath. Chest X-ray revealed right lower lobe atelectasis, while a chest computed tomography angiography (CTA) showed a large right hydrothorax with collapse of most of the right lung. A right lower lobe resection was performed and histologic and immunohistochemical analyses were consistent with a primary pulmonary epithelioid angiosarcoma. The patient was discharged, given supportive care, and died 12 days following her last operation.
原发性肺血管肉瘤是一种罕见的恶性肿瘤,具有侵袭性的临床行为和较差的预后。在此,我们报告一例罕见的原发性肺上皮样血管肉瘤病例,患者为一名59岁女性,最初表现为右侧胸痛和呼吸急促。胸部X线显示右下叶肺不张,而胸部计算机断层血管造影(CTA)显示右侧大量胸腔积液,右肺大部分萎陷。进行了右下叶切除术,组织学和免疫组织化学分析结果与原发性肺上皮样血管肉瘤相符。患者出院后接受支持性治疗,在最后一次手术后12天死亡。