Nakamura Masayuki, Hasegawa Hirotaka, Yasunaga Yoichi, Nakai Yudai, Umekawa Motoyuki, Saito Nobuhito
Departments of Neurosurgery, The University of Tokyo, Bunkyo, Tokyo, Japan.
Pathology, The University of Tokyo, Bunkyo, Tokyo, Japan.
J Neurosurg Case Lessons. 2024 Oct 14;8(16). doi: 10.3171/CASE24424.
Fibrous dysplasia (FD) is typically asymptomatic but is known to occasionally cause neurological symptoms such as visual disturbances. However, FD-associated abducens nerve palsy is extremely rare.
A 76-year-old woman had a left abducens nerve palsy due to mass effect on the abducens nerve at Dorello's canal caused by FD and its associated cyst, which was resolved by resection of the cyst through an endoscopic transnasal route.
Although FD is generally an asymptomatic lesion occurring in younger patients, it can occasionally cause abducens nerve palsy even in older patients. In particular, cystic degeneration within FD tends to trigger a mass effect and thus can require surgical decompression. https://thejns.org/doi/10.3171/CASE24424.
骨纤维异常增殖症(FD)通常无症状,但已知偶尔会引起神经症状,如视觉障碍。然而,FD相关的展神经麻痹极为罕见。
一名76岁女性因FD及其相关囊肿对Dorello管内展神经的占位效应而出现左侧展神经麻痹,通过鼻内镜经鼻切除囊肿后症状缓解。
尽管FD通常是发生在年轻患者中的无症状病变,但即使在老年患者中也可能偶尔导致展神经麻痹。特别是,FD内的囊性变倾向于引发占位效应,因此可能需要手术减压。https://thejns.org/doi/10.3171/CASE24424