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输血后紫癜:5例病例报告及发病机制与治疗综述

Post-transfusion purpura: a report of five patients and a review of the pathogenesis and management.

作者信息

Vogelsang G, Kickler T S, Bell W R

出版信息

Am J Hematol. 1986 Mar;21(3):259-67. doi: 10.1002/ajh.2830210305.

DOI:10.1002/ajh.2830210305
PMID:3946408
Abstract

We report five cases of post-transfusion purpura. Despite having profound thrombocytopenia, their management consisted only of steroid administration if serious bleeding was present. In one patient without bleeding, no specific therapy was given. This patient recovered uneventfully. Two patients died. One of these died from complicating illnesses rather than bleeding. The other suffered brain death, the result of a ruptured cerebral aneurysm. Four patients were PLA1 negative. The fifth patient had an antibody to an unidentified platelet-specific antigen.

摘要

我们报告了5例输血后紫癜病例。尽管存在严重血小板减少症,但如果出现严重出血,其治疗仅包括给予类固醇。在1例无出血的患者中,未给予特殊治疗。该患者顺利康复。2例患者死亡。其中1例死于并发症而非出血。另1例因脑动脉瘤破裂导致脑死亡。4例患者PLA1阴性。第5例患者有一种针对未鉴定的血小板特异性抗原的抗体。

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Post-transfusion purpura: a report of five patients and a review of the pathogenesis and management.输血后紫癜:5例病例报告及发病机制与治疗综述
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Post-transfusion purpura: case report.输血后紫癜:病例报告
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Post-transfusion purpura associated with unusual platelet antibody (anti-Pl-B1).与异常血小板抗体(抗Pl-B1)相关的输血后紫癜
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Studies on the pathophysiology of posttransfusion purpura.输血后紫癜的病理生理学研究。
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Clinical significance of platelet alloantibodies detected in immunofluorescence test (neonatal alloimmune thrombocytopenia and post-transfusion purpura).免疫荧光试验中检测到的血小板同种抗体的临床意义(新生儿同种免疫性血小板减少症和输血后紫癜)
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