Lv Chongqing, Feng Tao, Wang Shishou, Lin Chen
Department of General Surgery Shengli Oilfield Central Hospital Dongying China.
Department of Respiratory and Critical Care Medicine Shengli Oilfield Central Hospital Dongying China.
Respirol Case Rep. 2024 Dec 3;12(12):e70075. doi: 10.1002/rcr2.70075. eCollection 2024 Dec.
Bronchial artery-pulmonary artery fistula (BPF) is a rare vascular malformation of the bronchial arteries, associated with congenital heart disease, pulmonary hypertension, or pulmonary infections. It typically presents in adulthood and has a low incidence. Another rare vascular anomaly, bronchial Dieulafoy disease (BDD), is characterized by an abnormally developed artery within the submucosa of the bronchial tree. This condition is thought to arise from a combination of congenital dysplasia and chronic airway inflammation or injury. Both BPF and BDD are uncommon causes of hemoptysis, and their simultaneous occurrence is exceptionally rare. This report discusses a case of BPF complicated by BDD in a patient who presented with recurrent hemoptysis. The diagnosis was established through bronchial artery angiography, bronchoscopy, and surgical pathology. By examining the clinical features, imaging findings, and diagnostic criteria of these conditions, this case report aims to enhance clinicians' understanding of cryptogenic hemoptysis and provide valuable insights for clinical practice.
支气管动脉-肺动脉瘘(BPF)是一种罕见的支气管动脉血管畸形,与先天性心脏病、肺动脉高压或肺部感染有关。它通常在成年期出现,发病率较低。另一种罕见的血管异常,支气管迪厄拉富瓦病(BDD),其特征是支气管树黏膜下层内的动脉发育异常。这种情况被认为是由先天性发育异常与慢性气道炎症或损伤共同引起的。BPF和BDD都是咯血的罕见原因,它们同时发生极为罕见。本报告讨论了一例以反复咯血为表现的患者,该患者BPF合并BDD。通过支气管动脉血管造影、支气管镜检查和手术病理确诊。通过检查这些病症的临床特征、影像学表现和诊断标准,本病例报告旨在提高临床医生对隐源性咯血的认识,并为临床实践提供有价值的见解。