Deshpande Akshay, Rudzki Zbigniew, Bhat Jaideep, Pugh Matthew, Rose Susan, Paneesha Shankara
Department of Haematology, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK.
Department of Histopathology, University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK.
Case Rep Hematol. 2024 Nov 29;2024:8013335. doi: 10.1155/crh/8013335. eCollection 2024.
The unique histiocytic entity of indeterminate dendritic cell tumor (IDCT) is known to cause diagnostic conundrum and treatment dilemmas with no published consensus on either. We report a rare case of cutaneous IDCT with ETV3::NOAC2 rearrangement providing further evidence to its association with this condition. With its ease of administration and minimal side effects, PUVA therapy can be successfully used to treat cutaneous forms of IDCT.
不确定树突状细胞瘤（IDCT）独特的组织细胞实体已知会引发诊断难题和治疗困境，目前关于这两方面均未发表共识。我们报告了一例罕见的伴有ETV3::NOAC2重排的皮肤IDCT病例，为其与这种情况的关联提供了进一步证据。由于光化学疗法（PUVA）易于给药且副作用极小，可成功用于治疗皮肤型IDCT。
