• 文献检索
  • 文档翻译
  • 深度研究
  • 学术资讯
  • Suppr Zotero 插件Zotero 插件
  • 邀请有礼
  • 套餐&价格
  • 历史记录
应用&插件
Suppr Zotero 插件Zotero 插件浏览器插件Mac 客户端Windows 客户端微信小程序
定价
高级版会员购买积分包购买API积分包
服务
文献检索文档翻译深度研究API 文档MCP 服务
关于我们
关于 Suppr公司介绍联系我们用户协议隐私条款
关注我们

Suppr 超能文献

核心技术专利:CN118964589B侵权必究
粤ICP备2023148730 号-1Suppr @ 2026

文献检索

告别复杂PubMed语法,用中文像聊天一样搜索,搜遍4000万医学文献。AI智能推荐,让科研检索更轻松。

立即免费搜索

文件翻译

保留排版,准确专业,支持PDF/Word/PPT等文件格式,支持 12+语言互译。

免费翻译文档

深度研究

AI帮你快速写综述,25分钟生成高质量综述,智能提取关键信息,辅助科研写作。

立即免费体验

脑血管畸形:发病机制与治疗

Cerebral vascular malformations: pathogenesis and therapy.

作者信息

He Qiheng, Huo Ran, Sun Yingfan, Zheng Zhiyao, Xu Hongyuan, Zhao Shaozhi, Ni Yang, Yu Qifeng, Jiao Yuming, Zhang Wenqian, Zhao Jizong, Cao Yong

机构信息

Department of Neurosurgery Beijing Tiantan Hospital Capital Medical University Beijing China.

Basic and Translational Medicine Center China National Clinical Research Center for Neurological Diseases Beijing China.

出版信息

MedComm (2020). 2024 Dec 8;5(12):e70027. doi: 10.1002/mco2.70027. eCollection 2024 Dec.

DOI:10.1002/mco2.70027
PMID:39654683
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC11625509/
Abstract

Cerebral vascular malformations (CVMs), particularly cerebral cavernous malformations and cerebral arteriovenous malformations, pose significant neurological challenges due to their complex etiologies and clinical implications. Traditionally viewed as congenital conditions with structural abnormalities, CVMs have been treated primarily through resection, embolization, and stereotactic radiosurgery. While these approaches offer some efficacy, they often pose risks to neurological integrity due to their invasive nature. Advances in next-generation sequencing, particularly high-depth whole-exome sequencing and bioinformatics, have facilitated the identification of gene variants from neurosurgically resected CVMs samples. These advancements have deepened our understanding of CVM pathogenesis. Somatic mutations in key mechanistic pathways have been identified as causative factors, leading to a paradigm shift in CVM treatment. Additionally, recent progress in noninvasive and minimally invasive techniques, including gene imaging genomics, liquid biopsy, or endovascular biopsies (endovascular sampling of blood vessel lumens), has enabled the identification of gene variants associated with CVMs. These methods, in conjunction with clinical data, offer potential for early detection, dynamic monitoring, and targeted therapies that could be used as monotherapy or adjuncts to surgery. This review highlights advancements in CVM pathogenesis and precision therapies, outlining the future potential of precision medicine in CVM management.

摘要

脑血管畸形(CVMs),尤其是脑海绵状畸形和脑动静脉畸形,由于其复杂的病因和临床影响,带来了重大的神经学挑战。传统上,CVMs被视为具有结构异常的先天性疾病,主要通过切除、栓塞和立体定向放射外科进行治疗。虽然这些方法有一定疗效,但由于其侵入性,往往对神经完整性构成风险。新一代测序技术的进步,特别是高深度全外显子测序和生物信息学,有助于从神经外科切除的CVMs样本中识别基因变异。这些进展加深了我们对CVM发病机制的理解。关键机制途径中的体细胞突变已被确定为致病因素,导致CVM治疗发生范式转变。此外,非侵入性和微创技术的最新进展,包括基因成像基因组学、液体活检或血管内活检(血管腔的血管内采样),使得识别与CVMs相关的基因变异成为可能。这些方法与临床数据相结合,为早期检测、动态监测和靶向治疗提供了潜力,这些治疗可作为单一疗法或手术辅助手段。本综述强调了CVM发病机制和精准治疗方面的进展,概述了精准医学在CVM管理中的未来潜力。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/a007abc4c2fd/MCO2-5-e70027-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/ab3f120a728a/MCO2-5-e70027-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/17c1ee766145/MCO2-5-e70027-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/a007abc4c2fd/MCO2-5-e70027-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/ab3f120a728a/MCO2-5-e70027-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/17c1ee766145/MCO2-5-e70027-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/69ff/11625509/a007abc4c2fd/MCO2-5-e70027-g003.jpg

相似文献

1
Cerebral vascular malformations: pathogenesis and therapy.脑血管畸形:发病机制与治疗
MedComm (2020). 2024 Dec 8;5(12):e70027. doi: 10.1002/mco2.70027. eCollection 2024 Dec.
2
Cerebral Venous Malformations in a Chinese Population: Clinical Manifestations, Radiological Characteristics, and Long-Term Prognosis.中国人群中的脑静脉畸形:临床表现、影像学特征及长期预后
World Neurosurg. 2018 Dec;120:e472-e479. doi: 10.1016/j.wneu.2018.08.106. Epub 2018 Aug 25.
3
The future of open vascular neurosurgery: perspectives on cavernous malformations, AVMs, and bypasses for complex aneurysms.开放血管神经外科学的未来:海绵状血管畸形、动静脉畸形和复杂动脉瘤旁路手术的观点。
J Neurosurg. 2019 May 1;130(5):1409-1425. doi: 10.3171/2019.1.JNS182156.
4
Prevalence of Retinal Venous Malformations in Patients With Cerebral Cavernous or Arteriovenous Malformations.脑海绵状或动静脉畸形患者视网膜静脉畸形的患病率。
J Neuroophthalmol. 2024 Jun 1;44(2):226-231. doi: 10.1097/WNO.0000000000001974. Epub 2023 Aug 16.
5
Identification of Somatic Genetic Variants in Superficial Vascular Malformations by Liquid Biopsy in a Cohort of 88 Patients from a French Hospital.通过液体活检对法国一家医院88例患者队列中的浅表血管畸形进行体细胞遗传变异鉴定。
Mol Diagn Ther. 2025 May;29(3):367-380. doi: 10.1007/s40291-025-00770-0. Epub 2025 Feb 3.
6
Bleeding risk of cerebrovascular malformations in hereditary hemorrhagic telangiectasia.遗传性出血性毛细血管扩张症中脑血管畸形的出血风险
J Neurosurg. 2000 May;92(5):779-84. doi: 10.3171/jns.2000.92.5.0779.
7
Whole exome sequencing in 342 congenital cardiac left sided lesion cases reveals extensive genetic heterogeneity and complex inheritance patterns.对 342 例先天性心脏左侧病变病例进行全外显子组测序,揭示了广泛的遗传异质性和复杂的遗传模式。
Genome Med. 2017 Oct 31;9(1):95. doi: 10.1186/s13073-017-0482-5.
8
Clinical phenotype of adolescent and adult patients with extracranial vascular malformation.青少年和成年患者颅外血管畸形的临床表型。
J Vasc Surg Venous Lymphat Disord. 2023 Sep;11(5):1034-1044.e3. doi: 10.1016/j.jvsv.2023.03.012. Epub 2023 Apr 6.
9
Pathological considerations to irradiation of cavernous malformations.海绵状血管畸形放疗的病理学考量
Prog Neurol Surg. 2007;20:231-234. doi: 10.1159/000100122.
10
Reflections on the management of cerebral arteriovenous malformations.关于脑动静脉畸形治疗的思考
Surg Neurol. 1998 Sep;50(3):245-55; discussion 255-6. doi: 10.1016/s0090-3019(98)00082-2.

引用本文的文献

1
Cerebrovascular malformations different from AVMs in patients with hereditary hemorrhagic telangiectasia: a systematic review.遗传性出血性毛细血管扩张症患者中与动静脉畸形不同的脑血管畸形:一项系统综述
Neurol Sci. 2025 Sep 9. doi: 10.1007/s10072-025-08482-3.

本文引用的文献

1
The difference of functional MR imaging in evaluating outcome of patients with diffuse and compact brain arteriovenous malformation.弥散型与致密型脑动静脉畸形患者功能磁共振成像评估预后的差异。
Neurosurg Rev. 2024 Jul 24;47(1):347. doi: 10.1007/s10143-024-02593-9.
2
Sotorasib for Vascular Malformations Associated with G12C Mutation.索托拉西布治疗与 G12C 突变相关的血管畸形。
N Engl J Med. 2024 Jul 25;391(4):334-342. doi: 10.1056/NEJMoa2309160. Epub 2024 Jul 17.
3
Single-cell atlas of the human brain vasculature across development, adulthood and disease.
人类大脑血管系统在发育、成年和疾病过程中的单细胞图谱
Nature. 2024 Aug;632(8025):603-613. doi: 10.1038/s41586-024-07493-y. Epub 2024 Jul 10.
4
mTORC1 Signaling in Brain Endothelial Progenitors Contributes to CCM Pathogenesis.mTORC1 信号在脑内皮祖细胞中的作用促进 CCM 发病机制。
Circ Res. 2024 Aug 2;135(4):e94-e113. doi: 10.1161/CIRCRESAHA.123.324015. Epub 2024 Jul 3.
5
GNA14 and GNAQ somatic mutations cause spinal and intracranial extra-axial cavernous hemangiomas.GNA14 和 GNAQ 体细胞突变导致脊髓和颅内颅外硬膜外海绵状血管瘤。
Am J Hum Genet. 2024 Jul 11;111(7):1370-1382. doi: 10.1016/j.ajhg.2024.05.020. Epub 2024 Jun 24.
6
Prevalence, genetic and clinical characteristics in first-degree relatives of patients with familial cerebral cavernous malformations in China.中国家族性脑动静脉畸形患者一级亲属的患病率、遗传学及临床特征
Stroke Vasc Neurol. 2025 Feb 25;10(1):45-54. doi: 10.1136/svn-2023-003004.
7
Identifying potential (re)hemorrhage among sporadic cerebral cavernous malformations using machine learning.利用机器学习识别散发性脑海绵状血管畸形中的潜在(再)出血。
Sci Rep. 2024 May 14;14(1):11022. doi: 10.1038/s41598-024-61851-4.
8
MicroRNA-135b-5p Is a Pathologic Biomarker in the Endothelial Cells of Arteriovenous Malformations.miR-135b-5p 是动静脉畸形血管内皮细胞中的病理生物标志物。
Int J Mol Sci. 2024 Apr 30;25(9):4888. doi: 10.3390/ijms25094888.
9
Somatic Braf mutation in the cerebral endothelium induces brain arteriovenous malformations.大脑内皮细胞中的体细胞Braf突变会诱发脑动静脉畸形。
Angiogenesis. 2024 Aug;27(3):441-460. doi: 10.1007/s10456-024-09918-8. Epub 2024 May 3.
10
Cavernous Malformations of the Central Nervous System.中枢神经系统海绵状血管畸形
N Engl J Med. 2024 Mar 14;390(11):1022-1028. doi: 10.1056/NEJMra2305116.