Adnan Mohd, Ahmed Parwez, Kumar S Krishna, Khan Azad
Department of Orthopaedics, Teerthanker Mahaveer Medical College and Research Centre, Moradabad, Uttar Pradesh, India.
Department of Orthopaedics, Subharti Medical College and Hospital, Meerut, Uttar Pradesh, India.
J Orthop Case Rep. 2024 Dec;14(12):170-173. doi: 10.13107/jocr.2024.v14.i12.5062.
Primary leiomyosarcoma affecting the bone is an uncommon destructive tumor that primarily affects the elderly. If leiomyosarcoma is discovered in bone, it should be explored as a possible metastasis from a distant tumor. Surgical excision with broad margins is used as therapy.
A 50-year-old man reported to outpatient department with a 5-month chief complaint of a painful mass involving his left carpus that had grown. No history of trauma was present. Examination demonstrated a painful restriction of wrist motions, and ill-defined, immobile, tender hard mass measuring 5 × 3 cm along the ulnar border of the left wrist. All necessary investigations were done and were diagnosed as primary leiomyosarcoma of the distal ulna. Patient was managed surgically with resection with wide en bloc resection with a margin of at least 2 mm around the tumor and radioulnar stabilization with the help of 1 K-wire (2.5 mm). Post-operative period was uneventful.
Osseous leiomyosarcoma is an uncommon tumor, it should be evaluated in the diagnosis of any solely lytic aggressive osseous lesion in a middle age, Furthermore, the existence of extraosseous main lesions should be ruled out for its diagnosis. At present, surgery is the most effective therapy option.
原发性骨平滑肌肉瘤是一种罕见的侵袭性肿瘤，主要影响老年人。如果在骨中发现平滑肌肉瘤，应探究其是否为远处肿瘤的转移灶。治疗方法为广泛切缘的手术切除。
一名50岁男性因左腕部疼痛性肿块伴增大5个月就诊于门诊。无外伤史。检查发现腕关节活动疼痛受限，左腕尺侧缘有一5×3cm边界不清、固定、压痛的硬性肿块。完成了所有必要检查，诊断为尺骨远端原发性平滑肌肉瘤。患者接受了手术治疗，整块广泛切除肿瘤，肿瘤周围至少保留2mm切缘，并借助1根克氏针（2.5mm）进行桡尺骨固定。术后恢复顺利。
骨平滑肌肉瘤是一种罕见肿瘤，对于中年患者出现的任何单纯溶骨性侵袭性骨病变进行诊断时均应考虑到该病，此外，诊断时应排除骨外主要病变的存在。目前，手术是最有效的治疗选择。
